open access

Vol 88, No 1 (2020)
Guidelines / Expert consensus
Submitted: 2020-02-13
Accepted: 2020-02-13
Published online: 2020-02-28
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Guidelines of the Polish Respiratory Society for diagnosis and treatment of idiopathic pulmonary fibrosis

Wojciech Jerzy Piotrowski1, Iwona Bestry2, Adam J. Białas3, Piotr W. Boros4, Piotr Grzanka5, Ewa Jassem6, Dariusz Jastrzębski7, Dariusz Klimczak8, Renata Langfort9, Katarzyna Lewandowska10, Sebastian Majewski11, Magdalena M. Martusewicz-Boros12, Karina Onisch13, Elżbieta Puścińska14, Alicja Siemińska15, Małgorzata Sobiecka16, Małgorzata Szołkowska17, Elżbieta Wiatr18, Gracjan Wilczyński19, Dariusz Ziora20, Jan Kuś21
DOI: 10.5603/ARM.2020.0081
·
Pubmed: 32153010
·
Adv Respir Med 2020;88(1):42-94.
Affiliations
  1. Department of Pneumology and Allergy, Medical University of Lodz, Lodz, Poland
  2. Department of Radiology, National Tuberculosis and Lung Diseases Research Institute in Warsaw, Poland
  3. Department of Pathobiology of Respiratory Diseases, Medical University of Lodz, Poland
  4. Lung Pathophysiology Department, National Tuberculosis and Lung Diseases Research Institute in Warsaw, Poland
  5. Department of Radiology, Voivodeship Hospital in Opole, Poland
  6. Department of Allergology and Pneumonology, Medical University of Gdansk, Poland
  7. Department of Lung Diseases and Tuberculosis, Medical University of Silesia, Zabrze, Poland
  8. Patient, Polish Society for IPF Patients’ Support, Poland
  9. Department of Pathology, National Tuberculosis and Lung Diseases Research Institute in Warsaw
  10. First Lung Diseases Department, National Tuberculosis and Lung Diseases Research Institute in Warsaw, Poland
  11. Department of Pneumology and Allergy, Medical University of Lodz, Poland
  12. Third Lung Diseases and Oncology Department, National Tuberculosis and Lung Diseases Research Institute in Warsaw
  13. Department of Radiology, National Tuberculosis and Lung Diseases Research Institute in Warsaw, Poland
  14. Second Department of Respiratory Medicine, National Tuberculosis and Lung Diseases Research Institute in Warsaw, Poland
  15. Allergology Department, Medical University of Gdansk, Poland
  16. First Lung Diseases Department, National Tuberculosis and Lung Diseases Research Institute in Warsaw, Poland
  17. Department of Pathology, National Tuberculosis and Lung Diseases Research Institute in Warsaw
  18. Third Lung Diseases and Oncology Department, National Tuberculosis and Lung Diseases Research Institute in Warsaw
  19. Patient, not affiliated
  20. Department of Allergology and Pneumonology, Medical University of Gdansk, Poland
  21. First Lung Diseases Department, National Tuberculosis and Lung Diseases Research Institute in Warsaw, Poland

open access

Vol 88, No 1 (2020)
GUIDELINES
Submitted: 2020-02-13
Accepted: 2020-02-13
Published online: 2020-02-28

Abstract

Introduction: This document presents the guidelines of the Polish Respiratory Society (PTChP, Polskie Towarzystwo Chorób Płuc) for diagnosis and treatment of idiopathic pulmonary fibrosis (IPF), developed by a group of Polish experts.
Material and methods: The recommendations were developed in the form of answers to previously formulated questions concer-ning everyday diagnostic and therapeutic challenges. They were developed based on a current literature review using the Grading of Recommendations Assessment, Development and Evaluation (GRADE) methodology.
Results: We formulated 28 recommendations for diagnosis (8), pharmacological treatment (12) as well as non-pharma-cological and palliative therapy (8). The experts suggest that surgical lung biopsy (SLB) not be performed in patients with the probable usual interstitial pneumonia (UIP) pattern, with an appropriate clinical context and unanimous opinion of a  multidisciplinary team. The experts recommend using antifibrotic agents in IPF patients and suggest their use irrespective of the degree of functional impairment. As regards non-pharmacological and palliative treatment, strong re-commendations were formulated regarding pulmonary rehabilitation, oxygen therapy (in patients with chronic respiratory failure), preventive vaccinations as well as referring IPF patients to transplant centres. Table 1 presents an aggregate list of recommendations.
Conclusions: The Polish Respiratory Society Working Group developed guidelines for IPF diagnosis and treatment.

Abstract

Introduction: This document presents the guidelines of the Polish Respiratory Society (PTChP, Polskie Towarzystwo Chorób Płuc) for diagnosis and treatment of idiopathic pulmonary fibrosis (IPF), developed by a group of Polish experts.
Material and methods: The recommendations were developed in the form of answers to previously formulated questions concer-ning everyday diagnostic and therapeutic challenges. They were developed based on a current literature review using the Grading of Recommendations Assessment, Development and Evaluation (GRADE) methodology.
Results: We formulated 28 recommendations for diagnosis (8), pharmacological treatment (12) as well as non-pharma-cological and palliative therapy (8). The experts suggest that surgical lung biopsy (SLB) not be performed in patients with the probable usual interstitial pneumonia (UIP) pattern, with an appropriate clinical context and unanimous opinion of a  multidisciplinary team. The experts recommend using antifibrotic agents in IPF patients and suggest their use irrespective of the degree of functional impairment. As regards non-pharmacological and palliative treatment, strong re-commendations were formulated regarding pulmonary rehabilitation, oxygen therapy (in patients with chronic respiratory failure), preventive vaccinations as well as referring IPF patients to transplant centres. Table 1 presents an aggregate list of recommendations.
Conclusions: The Polish Respiratory Society Working Group developed guidelines for IPF diagnosis and treatment.

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Keywords

diagnosis; idiopathic pulmonary fibrosis; treatment; differentiation; usual interstitial pneumonia

About this article
Title

Guidelines of the Polish Respiratory Society for diagnosis and treatment of idiopathic pulmonary fibrosis

Journal

Advances in Respiratory Medicine

Issue

Vol 88, No 1 (2020)

Article type

Guidelines / Expert consensus

Pages

42-94

Published online

2020-02-28

Page views

3102

Article views/downloads

2120

DOI

10.5603/ARM.2020.0081

Pubmed

32153010

Bibliographic record

Adv Respir Med 2020;88(1):42-94.

Keywords

diagnosis
idiopathic pulmonary fibrosis
treatment
differentiation
usual interstitial pneumonia

Authors

Wojciech Jerzy Piotrowski
Iwona Bestry
Adam J. Białas
Piotr W. Boros
Piotr Grzanka
Ewa Jassem
Dariusz Jastrzębski
Dariusz Klimczak
Renata Langfort
Katarzyna Lewandowska
Sebastian Majewski
Magdalena M. Martusewicz-Boros
Karina Onisch
Elżbieta Puścińska
Alicja Siemińska
Małgorzata Sobiecka
Małgorzata Szołkowska
Elżbieta Wiatr
Gracjan Wilczyński
Dariusz Ziora
Jan Kuś

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