open access

Vol 88, No 1 (2020)
GUIDELINES
Published online: 2020-02-28
Submitted: 2020-02-13
Accepted: 2020-02-13
Get Citation

Guidelines of the Polish Respiratory Society for diagnosis and treatment of idiopathic pulmonary fibrosis

Wojciech Jerzy Piotrowski, Iwona Bestry, Adam J. Białas, Piotr W. Boros, Piotr Grzanka, Ewa Jassem, Dariusz Jastrzębski, Dariusz Klimczak, Renata Langfort, Katarzyna Lewandowska, Sebastian Majewski, Magdalena M. Martusewicz-Boros, Karina Onisch, Elżbieta Puścińska, Alicja Siemińska, Małgorzata Sobiecka, Małgorzata Szołkowska, Elżbieta Wiatr, Gracjan Wilczyński, Dariusz Ziora, Jan Kuś
DOI: 10.5603/ARM.2020.0081
·
Pubmed: 32153010
·
Adv Respir Med 2020;88(1):42-94.

open access

Vol 88, No 1 (2020)
GUIDELINES
Published online: 2020-02-28
Submitted: 2020-02-13
Accepted: 2020-02-13

Abstract

Introduction: This document presents the guidelines of the Polish Respiratory Society (PTChP, Polskie Towarzystwo Chorób Płuc) for diagnosis and treatment of idiopathic pulmonary fibrosis (IPF), developed by a group of Polish experts.
Material and methods: The recommendations were developed in the form of answers to previously formulated questions concer-ning everyday diagnostic and therapeutic challenges. They were developed based on a current literature review using the Grading of Recommendations Assessment, Development and Evaluation (GRADE) methodology.
Results: We formulated 28 recommendations for diagnosis (8), pharmacological treatment (12) as well as non-pharma-cological and palliative therapy (8). The experts suggest that surgical lung biopsy (SLB) not be performed in patients with the probable usual interstitial pneumonia (UIP) pattern, with an appropriate clinical context and unanimous opinion of a  multidisciplinary team. The experts recommend using antifibrotic agents in IPF patients and suggest their use irrespective of the degree of functional impairment. As regards non-pharmacological and palliative treatment, strong re-commendations were formulated regarding pulmonary rehabilitation, oxygen therapy (in patients with chronic respiratory failure), preventive vaccinations as well as referring IPF patients to transplant centres. Table 1 presents an aggregate list of recommendations.
Conclusions: The Polish Respiratory Society Working Group developed guidelines for IPF diagnosis and treatment.

Abstract

Introduction: This document presents the guidelines of the Polish Respiratory Society (PTChP, Polskie Towarzystwo Chorób Płuc) for diagnosis and treatment of idiopathic pulmonary fibrosis (IPF), developed by a group of Polish experts.
Material and methods: The recommendations were developed in the form of answers to previously formulated questions concer-ning everyday diagnostic and therapeutic challenges. They were developed based on a current literature review using the Grading of Recommendations Assessment, Development and Evaluation (GRADE) methodology.
Results: We formulated 28 recommendations for diagnosis (8), pharmacological treatment (12) as well as non-pharma-cological and palliative therapy (8). The experts suggest that surgical lung biopsy (SLB) not be performed in patients with the probable usual interstitial pneumonia (UIP) pattern, with an appropriate clinical context and unanimous opinion of a  multidisciplinary team. The experts recommend using antifibrotic agents in IPF patients and suggest their use irrespective of the degree of functional impairment. As regards non-pharmacological and palliative treatment, strong re-commendations were formulated regarding pulmonary rehabilitation, oxygen therapy (in patients with chronic respiratory failure), preventive vaccinations as well as referring IPF patients to transplant centres. Table 1 presents an aggregate list of recommendations.
Conclusions: The Polish Respiratory Society Working Group developed guidelines for IPF diagnosis and treatment.

Get Citation

Keywords

diagnosis; idiopathic pulmonary fibrosis; treatment; differentiation; usual interstitial pneumonia

About this article
Title

Guidelines of the Polish Respiratory Society for diagnosis and treatment of idiopathic pulmonary fibrosis

Journal

Advances in Respiratory Medicine

Issue

Vol 88, No 1 (2020)

Pages

42-94

Published online

2020-02-28

DOI

10.5603/ARM.2020.0081

Pubmed

32153010

Bibliographic record

Adv Respir Med 2020;88(1):42-94.

Keywords

diagnosis
idiopathic pulmonary fibrosis
treatment
differentiation
usual interstitial pneumonia

Authors

Wojciech Jerzy Piotrowski
Iwona Bestry
Adam J. Białas
Piotr W. Boros
Piotr Grzanka
Ewa Jassem
Dariusz Jastrzębski
Dariusz Klimczak
Renata Langfort
Katarzyna Lewandowska
Sebastian Majewski
Magdalena M. Martusewicz-Boros
Karina Onisch
Elżbieta Puścińska
Alicja Siemińska
Małgorzata Sobiecka
Małgorzata Szołkowska
Elżbieta Wiatr
Gracjan Wilczyński
Dariusz Ziora
Jan Kuś

Important: This website uses cookies. More >>

The cookies allow us to identify your computer and find out details about your last visit. They remembering whether you've visited the site before, so that you remain logged in - or to help us work out how many new website visitors we get each month. Most internet browsers accept cookies automatically, but you can change the settings of your browser to erase cookies or prevent automatic acceptance if you prefer.

Czasopismo Pneumonologia i Alergologia Polska dostęne jest również w Ikamed - księgarnia medyczna

Wydawcą serwisu jest "Via Medica sp. z o.o." sp.k., ul. Świętokrzyska 73, 80–180 Gdańsk

tel.:+48 58 320 94 94, faks:+48 58 320 94 60, e-mail: viamedica@viamedica.pl