Rzadkie choroby limfoproliferacyjne ujęte w 5. wersji klasyfikacji WHO
Streszczenie
Artykuł poświęcono nowo wyłonionej grupie chorób limfoproliferacyjnych, uwzględnionej w 5. klasyfikacji WHO. To zagadnienia medyczne z pogranicza obszaru specjalizacji hematologa. Dotyczą głównie chorób rzadkich oraz tych, których diagnozą i leczeniem zajmują się głównie specjaliści reumatolodzy. Pomimo braku charakteru klonalnego opisywanych limfoproliferacji, ich przebieg kliniczny może być agresywny, wymagając szybkiego wprowadzenia specjalistycznej terapii. Przede wszystkim jednak wyzwaniem pozostaje błyskawiczna i precyzyjna diagnoza. W artykule przedstawiono cechy kliniczne i laboratoryjne poszczególnych jednostek chorobowych, dokonano także przeglądu metod ich leczenia.
Słowa kluczowe: choroba Castlemanachoroby IgG4-zależnechoroby limfoproliferacyjne
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