Tom 16, Nr 3 (2019)
Nadciśnienie płucne
Opublikowany online: 2019-09-24
Zakrzepowo-zatorowe nadciśnienie płucne — aktualny stan wiedzy
Choroby Serca i Naczyń 2019;16(3):151-157.
Streszczenie
Przewlekłe zakrzepowo-zatorowe nadciśnienie
płucne (CTEPH) stanowi 4. grupę nadciśnienia
płucnego według klasyfikacji World Health Organization.
Rozwija się zarówno u osób po przebytym
incydencie ostrej zatorowości płucnej (PE),
jak i u chorych, którzy nigdy nie przebyli jawnego
epizodu PE czy zakrzepicy żył głębokich.
Nieleczona choroba prowadzi do niewydolności
prawokomorowej i zgonu. Choć „złotym standardem”
leczenia CTEPH pozostaje endarterektomia
płucna (PEA), to ostatnie lata przyniosły znaczący
postęp w zakresie rozwoju alternatywnych metod
leczenia dla chorych niebędących kandydatami
do PEA. Niniejszy artykuł stanowi podsumowanie
aktualnego stanu wiedzy na temat patofizjologii
oraz leczenia tej jednostki chorobowej.
Słowa kluczowe: zakrzepowo-zatorowe nadciśnienie płucnezatorowość płucnaendarterektomia płucnaangioplastyka balonowa
Referencje
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