open access

Vol 15, No 2 (2013)
Case reports
Published online: 2014-09-23
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Malignant peripheral nerve sheath tumour

Rafał Boczej, Ryszard Walas, Marek Motyka
Chirurgia Polska 2013;15(2):141-145.

open access

Vol 15, No 2 (2013)
Case reports
Published online: 2014-09-23

Abstract

Sarcomas belong to a diverse group of mesenchymal tumours. They make up for 1% malignant tumours in adults population. There are estimated 1500–2000 new cases of soft tissue and bone sarcomas yearly in Poland. About 5–10% of all sarcomas are malignant peripheral nerve sheath tumours (MPNST).
Malignant peripheral nerve sheath tumours (MPNST) are usually located within the torso (about 50% cases), more seldom within the extremities (30%) or head and neck (20%). MPNST is a rare condition, which is why no guidelines regarding the diagnostic process and treatment can be found in literature.
The modern treatment for soft tissue sarcomas involves a combination of surgery and radiotherapy, and in some cases chemotherapy. A cure can only be reached by a radical removal of the tumour. A good cooperation between the surgeon and the radiotherapy oncologist increases the chances of successful treatment. At the same time the importance of immunohistochemical assessment should be stressed, with the result determining the further course of therapy.

Abstract

Sarcomas belong to a diverse group of mesenchymal tumours. They make up for 1% malignant tumours in adults population. There are estimated 1500–2000 new cases of soft tissue and bone sarcomas yearly in Poland. About 5–10% of all sarcomas are malignant peripheral nerve sheath tumours (MPNST).
Malignant peripheral nerve sheath tumours (MPNST) are usually located within the torso (about 50% cases), more seldom within the extremities (30%) or head and neck (20%). MPNST is a rare condition, which is why no guidelines regarding the diagnostic process and treatment can be found in literature.
The modern treatment for soft tissue sarcomas involves a combination of surgery and radiotherapy, and in some cases chemotherapy. A cure can only be reached by a radical removal of the tumour. A good cooperation between the surgeon and the radiotherapy oncologist increases the chances of successful treatment. At the same time the importance of immunohistochemical assessment should be stressed, with the result determining the further course of therapy.
Get Citation

Keywords

malignant peripheral nerve sheath tumours (MPNST), surgical treatment

About this article
Title

Malignant peripheral nerve sheath tumour

Journal

Chirurgia Polska (Polish Surgery)

Issue

Vol 15, No 2 (2013)

Pages

141-145

Published online

2014-09-23

Bibliographic record

Chirurgia Polska 2013;15(2):141-145.

Keywords

malignant peripheral nerve sheath tumours (MPNST)
surgical treatment

Authors

Rafał Boczej
Ryszard Walas
Marek Motyka

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