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Malignant peripheral nerve sheath tumour
open access
Abstract
Malignant peripheral nerve sheath tumours (MPNST) are usually located within the torso (about 50% cases), more seldom within the extremities (30%) or head and neck (20%). MPNST is a rare condition, which is why no guidelines regarding the diagnostic process and treatment can be found in literature.
The modern treatment for soft tissue sarcomas involves a combination of surgery and radiotherapy, and in some cases chemotherapy. A cure can only be reached by a radical removal of the tumour. A good cooperation between the surgeon and the radiotherapy oncologist increases the chances of successful treatment. At the same time the importance of immunohistochemical assessment should be stressed, with the result determining the further course of therapy.
Abstract
Malignant peripheral nerve sheath tumours (MPNST) are usually located within the torso (about 50% cases), more seldom within the extremities (30%) or head and neck (20%). MPNST is a rare condition, which is why no guidelines regarding the diagnostic process and treatment can be found in literature.
The modern treatment for soft tissue sarcomas involves a combination of surgery and radiotherapy, and in some cases chemotherapy. A cure can only be reached by a radical removal of the tumour. A good cooperation between the surgeon and the radiotherapy oncologist increases the chances of successful treatment. At the same time the importance of immunohistochemical assessment should be stressed, with the result determining the further course of therapy.
Keywords
malignant peripheral nerve sheath tumours (MPNST), surgical treatment


Title
Malignant peripheral nerve sheath tumour
Journal
Chirurgia Polska (Polish Surgery)
Issue
Pages
141-145
Published online
2014-09-23
Bibliographic record
Chirurgia Polska 2013;15(2):141-145.
Keywords
malignant peripheral nerve sheath tumours (MPNST)
surgical treatment
Authors
Rafał Boczej
Ryszard Walas
Marek Motyka