open access

Vol 21, No 4 (2016)
Special Issue Papers
Published online: 2016-07-01
Submitted: 2014-10-07
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Treatment of endolymphatic sac tumour (Papillary adenocarcinoma) of the temporal bone

Arturo Mario Poletti, Siba Prasad Dubey, Giovanni Colombo, Giovanni Cugini, Antonio Mazzoni
DOI: 10.1016/j.rpor.2015.06.003
·
Rep Pract Oncol Radiother 2016;21(4):391-394.

open access

Vol 21, No 4 (2016)
Special Issue Papers
Published online: 2016-07-01
Submitted: 2014-10-07

Abstract

Aim

To define a better treatment of sporadic endolymphatic sac tumours (ELST) analysing our experience and literature available data.

Background

ELST can arise as sporadic case (rare) or as a part of von Hippel–Lindau (VHL) disease. It is a low grade malignancy with local spread by continuity.

Materials and methods

we described our experience with 7 cases with up to date follow up.

Results

Five cases were free of disease after first surgical procedure. One case had recurrence in the temporal lobe after 12 years. One case had two surgical procedures followed by irradiation and died five years after radiotherapy with a slow disease progression.

Conclusion

With increasing expertise in the skull base surgery, complete tumour excisions are achieved in majority of the more recent cases and appear to be the treatment of choice. External irradiation is also used as palliative measures with doubtful effectiveness. Some recent reports showed encouraging results with gamma knife radiosurgery.

Abstract

Aim

To define a better treatment of sporadic endolymphatic sac tumours (ELST) analysing our experience and literature available data.

Background

ELST can arise as sporadic case (rare) or as a part of von Hippel–Lindau (VHL) disease. It is a low grade malignancy with local spread by continuity.

Materials and methods

we described our experience with 7 cases with up to date follow up.

Results

Five cases were free of disease after first surgical procedure. One case had recurrence in the temporal lobe after 12 years. One case had two surgical procedures followed by irradiation and died five years after radiotherapy with a slow disease progression.

Conclusion

With increasing expertise in the skull base surgery, complete tumour excisions are achieved in majority of the more recent cases and appear to be the treatment of choice. External irradiation is also used as palliative measures with doubtful effectiveness. Some recent reports showed encouraging results with gamma knife radiosurgery.

Get Citation

Keywords

Endolymphatic sac; Tumour; Temporal bone; Surgery; Papillary adenocarcinoma

About this article
Title

Treatment of endolymphatic sac tumour (Papillary adenocarcinoma) of the temporal bone

Journal

Reports of Practical Oncology and Radiotherapy

Issue

Vol 21, No 4 (2016)

Pages

391-394

Published online

2016-07-01

DOI

10.1016/j.rpor.2015.06.003

Bibliographic record

Rep Pract Oncol Radiother 2016;21(4):391-394.

Keywords

Endolymphatic sac
Tumour
Temporal bone
Surgery
Papillary adenocarcinoma

Authors

Arturo Mario Poletti
Siba Prasad Dubey
Giovanni Colombo
Giovanni Cugini
Antonio Mazzoni

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