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Vol 5, No 4 (2019)
Review paper
Published online: 2020-02-05
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Heart in systemic sclerosis — pathogenesis and diagnosis based on new imaging methods

Żaneta Smoleńska1, Ewa Puzio1, Karolina Dorniak1, Marta Grono-Burakowska1, Zbigniew Zdrojewski1
DOI: 10.5603/FR.2019.0020
·
Forum Reumatol 2019;5(4):181-189.
Affiliations
  1. Klinika Neurologii Rozwojowej, Katedra Neurologii, Gdański Uniwersytet Medyczny, Poland

open access

Vol 5, No 4 (2019)
Review
Published online: 2020-02-05

Abstract

The heart is one of the most frequently involved organs in systemic sclerosis. Myocardial fibrosis is the most common pathological change; it is caused by changes in microcirculation, inflammation and repair processes. In most systemic sclerosis patients, the course of cardiac involvement is subclinical, especially in the early stages of the disease. This article discusses the mechanisms which lead to cardiac injury, its various clinical forms as well as procedures with respect to diagnosis, with a particular emphasis on new tools, such as echocardiography and cardiac magnetic resonance.

Forum Reumatol. 2019, tom 5, nr 4: 181–189

Abstract

The heart is one of the most frequently involved organs in systemic sclerosis. Myocardial fibrosis is the most common pathological change; it is caused by changes in microcirculation, inflammation and repair processes. In most systemic sclerosis patients, the course of cardiac involvement is subclinical, especially in the early stages of the disease. This article discusses the mechanisms which lead to cardiac injury, its various clinical forms as well as procedures with respect to diagnosis, with a particular emphasis on new tools, such as echocardiography and cardiac magnetic resonance.

Forum Reumatol. 2019, tom 5, nr 4: 181–189

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Keywords

systemic sclerosis; cardiac involvement; diagnostic methods

About this article
Title

Heart in systemic sclerosis — pathogenesis and diagnosis based on new imaging methods

Journal

Rheumatology Forum

Issue

Vol 5, No 4 (2019)

Article type

Review paper

Pages

181-189

Published online

2020-02-05

Page views

717

Article views/downloads

575

DOI

10.5603/FR.2019.0020

Bibliographic record

Forum Reumatol 2019;5(4):181-189.

Keywords

systemic sclerosis
cardiac involvement
diagnostic methods

Authors

Żaneta Smoleńska
Ewa Puzio
Karolina Dorniak
Marta Grono-Burakowska
Zbigniew Zdrojewski

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