Vol 3, No 1 (2017)
Case report
Published online: 2017-04-19
Cryoglobulinemia in the course of a primary Sjögren’s syndrome
Forum Reumatol 2017;3(1):35-38.
Abstract
A 58-year-old woman with primary Sjögren’s syndrome (pSS), peripheral neuropathy and positive serum cryoglobulin was admitted for evaluation of purpura on her skin. Cryoglobulinemic vasculitis was diagnosed based on clinical and laboratory findings . There was no response to cyclophosphamide pulse therapy, steroid therapy and cyclosporine. We presente the discussion about cryoglobulinemic vasculitis in pSS, the overall prognosis (B-cell lymphomas) and differential diagnosis.
Keywords: primary Sjögren’s syndromecryoglobulinspurpuralymphomas
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