Tom 20, Nr 4 (2024)
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Opublikowany online: 2025-02-12
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Eksport do Mediów Społecznościowych

Eksport do Mediów Społecznościowych

Wtrętowe zapalenie mięśni – opis przypadku z odniesieniem do kryteriów diagnostycznych z 2024 roku

Anna Pieniaka1, Marta Nowakowska-Kotas1, Magdalena Koszewicz1, Katarzyna Haczkiewicz-Leśniak2, Michał Kulus2, Marzenna Podhorska-Okołów2, Sławomir Budrewicz1
DOI: 10.5603/ppn.103648
Pol. Przegl. Neurol 2024;20(4):216-225.

Streszczenie

W pracy opisano przypadek 82-letniej kobiety z zaburzeniami chodu, osłabieniem kończyn dolnych oraz z dysfagią, u której na podstawie badań neurofizjologicznych, biopsji mięśnia i wyników laboratoryjnych rozpoznano wtrętowe zapalenie mięśni (IBM, inclusion body myositis). W artykule omówiono najnowsze koncepcje IBM jako choroby autoimmunologicznej ale także zwyrodnieniowej. Wtrętowe zapalenie mięśni cechuje się stopniowym osłabieniem mięśni, często asymetrycznym, z zajęciem głębokich zginaczy palców, prostowników kolan. Choć spotykane są i inne, mniej typowe wzorce zajęcia mięśni. Zagadnienie badań pomocniczych niezbędnych do przeprowadzenia diagnostyki różnicowej zostało omówione na podstawie najnowszych kryteriów diagnostycznych wtrętowego zapalenia mięśni z 2024 roku.

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