open access

Vol 4 (2019): Continuous Publishing
CASE REPORTS
Published online: 2019-07-31
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Refractory macular edema in X-linked juvenile retinoschisis

Rashed Mustafa Nazzal, Robert Rejdak
DOI: 10.5603/OJ.2019.0005
·
Ophthalmol J 2019;4:46-48.

open access

Vol 4 (2019): Continuous Publishing
CASE REPORTS
Published online: 2019-07-31

Abstract

X-linked juvenile retinoschisis (XLRS) is one of the most common X-linked inherited, bilateral vitreoretinal dystrophies
affecting males in the first two decades of life. In this article, we present a case report of a young man who
presented with gradual decrease in visual acuity in both eyes that was attributed to macular edema and foveal schisis
in the inner retinal layers. He was investigated by appropriate ocular images which were consistent with a diagnosis
of XLRS. He was treated by anti-vascular endothelial growth factor (anti-VEGF) intravitreal injection, dorzolamide
eye drops and intravitreal steroids injection without improvement.

Abstract

X-linked juvenile retinoschisis (XLRS) is one of the most common X-linked inherited, bilateral vitreoretinal dystrophies
affecting males in the first two decades of life. In this article, we present a case report of a young man who
presented with gradual decrease in visual acuity in both eyes that was attributed to macular edema and foveal schisis
in the inner retinal layers. He was investigated by appropriate ocular images which were consistent with a diagnosis
of XLRS. He was treated by anti-vascular endothelial growth factor (anti-VEGF) intravitreal injection, dorzolamide
eye drops and intravitreal steroids injection without improvement.

Get Citation

Keywords

retinoschisis; macular edema; juvenile; carbonic anhydrase inhibitors; vascular endothelial growth factor

About this article
Title

Refractory macular edema in X-linked juvenile retinoschisis

Journal

Ophthalmology Journal

Issue

Vol 4 (2019): Continuous Publishing

Pages

46-48

Published online

2019-07-31

DOI

10.5603/OJ.2019.0005

Bibliographic record

Ophthalmol J 2019;4:46-48.

Keywords

retinoschisis
macular edema
juvenile
carbonic anhydrase inhibitors
vascular endothelial growth factor

Authors

Rashed Mustafa Nazzal
Robert Rejdak

References (13)
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