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Intravitreal anti-VEGF therapy in macular oedema secondary to racemose haemangiomatosis of the retina
- Department of Vitreoretinal Surgery, Medical University in Lublin, Lublin, Poland, Poland
open access
Abstract
Racemose haemangiomatosis of the retina is a sporadic, mostly unilateral, congenital arteriovenous malformation (AVM), comprising abnormal junctions between arteries and veins that omit capillaries. Typically, vascular malformations are asymptomatic and incidentally discovered. Advanced changes may be related to the presence of subretinal fluid and exudates, even though these lesions are classified as benign. Many complications can lead to severe or permanent visual impairment. Direct methods of treatment of primary retinal vascular anomalies have not been developed yet. The aim of this case report is to present the anti-VEGF therapy in the treatment macular oedema secondary to racemose haemangioma.
Abstract
Racemose haemangiomatosis of the retina is a sporadic, mostly unilateral, congenital arteriovenous malformation (AVM), comprising abnormal junctions between arteries and veins that omit capillaries. Typically, vascular malformations are asymptomatic and incidentally discovered. Advanced changes may be related to the presence of subretinal fluid and exudates, even though these lesions are classified as benign. Many complications can lead to severe or permanent visual impairment. Direct methods of treatment of primary retinal vascular anomalies have not been developed yet. The aim of this case report is to present the anti-VEGF therapy in the treatment macular oedema secondary to racemose haemangioma.
Keywords
racemose haemangiomatosis, anti-VEGF, macular oedema, intravitreal injection
Title
Intravitreal anti-VEGF therapy in macular oedema secondary to racemose haemangiomatosis of the retina
Journal
Issue
Article type
Case report
Pages
58-60
Published online
2017-06-28
Page views
622
Article views/downloads
1261
DOI
Bibliographic record
Ophthalmol J 2017;2(2):58-60.
Keywords
racemose haemangiomatosis
anti-VEGF
macular oedema
intravitreal injection
Authors
Magdalena Tylus
Jerzy Mackiewicz
Joanna Dolar-Szczasny
Anna Święch-Zubilewicz
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