Vol 2, No 2 (2017)
Case report
Published online: 2017-06-28

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Intravitreal anti-VEGF therapy in macular oedema secondary to racemose haemangiomatosis of the retina

Magdalena Tylus1, Jerzy Mackiewicz1, Joanna Dolar-Szczasny1, Anna Święch-Zubilewicz1
Ophthalmol J 2017;2(2):58-60.


Racemose haemangiomatosis of the retina is a sporadic, mostly unilateral, congenital arteriovenous malformation (AVM), comprising abnormal junctions between arteries and veins that omit capillaries. Typically, vascular malformations are asymptomatic and incidentally discovered. Advanced changes may be related to the presence of subretinal fluid and exudates, even though these lesions are classified as benign. Many complications can lead to severe or permanent visual impairment. Direct methods of treatment of primary retinal vascular anomalies have not been developed yet. The aim of this case report is to present the anti-VEGF therapy in the treatment macular oedema secondary to racemose haemangioma.


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