open access

Vol 51, No 2 (2017)
Case reports
Submitted: 2016-09-23
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The Heidenhain variant of Creutzfeldt–Jakob disease and concomitant tau pathology: A case report

Edvard Ehler, Michael Pipka, Alena Meleková, Petra Mandysová, Silvie Johanidesová, Radoslav Matěj, Robert Rusina
DOI: 10.1016/j.pjnns.2017.01.011
·
Neurol Neurochir Pol 2017;51(2):197-200.

open access

Vol 51, No 2 (2017)
Case reports
Submitted: 2016-09-23

Abstract

•The Heidenhain form of CJD is a rare variant with predominantly visual symptoms.•Clinical findings correlate with involvement of posterior cortical regions.•MRI found typical cortical hyperintensities in the occipital regions.•Neuropathology revealed histopathological changes consistent with prion disease.•Hyperphosphorylated tau deposits were an additional and interesting finding in our case.

Abstract

•The Heidenhain form of CJD is a rare variant with predominantly visual symptoms.•Clinical findings correlate with involvement of posterior cortical regions.•MRI found typical cortical hyperintensities in the occipital regions.•Neuropathology revealed histopathological changes consistent with prion disease.•Hyperphosphorylated tau deposits were an additional and interesting finding in our case.

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Keywords

Prion, Creutzfeldt–Jakob disease, Visuospatial dysfunction, Heidenhain variant

About this article
Title

The Heidenhain variant of Creutzfeldt–Jakob disease and concomitant tau pathology: A case report

Journal

Neurologia i Neurochirurgia Polska

Issue

Vol 51, No 2 (2017)

Pages

197-200

DOI

10.1016/j.pjnns.2017.01.011

Bibliographic record

Neurol Neurochir Pol 2017;51(2):197-200.

Keywords

Prion
Creutzfeldt–Jakob disease
Visuospatial dysfunction
Heidenhain variant

Authors

Edvard Ehler
Michael Pipka
Alena Meleková
Petra Mandysová
Silvie Johanidesová
Radoslav Matěj
Robert Rusina

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