open access

Vol 50, No 1 (2016)
Case reports
Submitted: 2015-08-07
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Unilateral progressive muscular atrophy with fast symptoms progression

Andrzej Bogucki, Justyna Pigońska, Iwona Szadkowska, Agata Gajos
DOI: 10.1016/j.pjnns.2015.10.009
·
Neurol Neurochir Pol 2016;50(1):52-54.

open access

Vol 50, No 1 (2016)
Case reports
Submitted: 2015-08-07

Abstract

Progressive muscular atrophy (PMA), or the lower motor neuron disease, is a sporadic disorder characterized by onset in adulthood, pure lower motor neuron involvement and relatively benign course. Muscle atrophy and weakness may be symmetrical or asymmetrical, but they are always bilateral. We present a male patient with exclusively left-side flaccid paresis due to lower motor neuron disease without electromyographic evidence of neurogenic lesion of contralateral muscles and with no signs of corticospinal tracts involvement. The rapid disease progression was typical of the generalized phenotype of PMA and it suggested the relation to the aggressive course of classical ALS.

Abstract

Progressive muscular atrophy (PMA), or the lower motor neuron disease, is a sporadic disorder characterized by onset in adulthood, pure lower motor neuron involvement and relatively benign course. Muscle atrophy and weakness may be symmetrical or asymmetrical, but they are always bilateral. We present a male patient with exclusively left-side flaccid paresis due to lower motor neuron disease without electromyographic evidence of neurogenic lesion of contralateral muscles and with no signs of corticospinal tracts involvement. The rapid disease progression was typical of the generalized phenotype of PMA and it suggested the relation to the aggressive course of classical ALS.

Get Citation

Keywords

Motor neuron disease, Progressive muscular atrophy, Unilateral symptoms, Electromyography

About this article
Title

Unilateral progressive muscular atrophy with fast symptoms progression

Journal

Neurologia i Neurochirurgia Polska

Issue

Vol 50, No 1 (2016)

Pages

52-54

DOI

10.1016/j.pjnns.2015.10.009

Bibliographic record

Neurol Neurochir Pol 2016;50(1):52-54.

Keywords

Motor neuron disease
Progressive muscular atrophy
Unilateral symptoms
Electromyography

Authors

Andrzej Bogucki
Justyna Pigońska
Iwona Szadkowska
Agata Gajos

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