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Solitary fibrous tumour with intramedullary component: Case report and review of the literature
- Department of Neurosurgery, Hôpital de Sion, Réseau Santé Valais, Sion, Switzerland
- Department of Pathology, Institut Central des Hôpitaux Valaisans, Sion, Switzerland
- Department of Radiology, Hôpital de Sion, Réseau Santé Valais, Sion, Switzerland
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Abstract
Solitary fibrous tumours (SFTs) are rare WHO grade I mesenchymal neoplasms that were first described in the visceral pleura. A wide variety of locations of SFT have been reported but only twelve cases of intramedullary solitary fibrous tumour. We report a case of thoracic spinal cord SFT.
A 49-year-old woman presented with clinical signs of dorsal myelopathy. Magnetic resonance imaging revealed an intradural mass at level T9–T10 which showed imaging features consistent both for an intra- and an extramedullary location of a solid tumour. Imaging findings were confirmed during surgery which was successful in resecting the extramedullary component. The intramedullary component could only be partially resected.
Solitary fibrous tumour is a rare pathological entity in the central nervous system. The course of intramedullary SFT is unknown and careful long-term follow-up is recommended.
Abstract
Solitary fibrous tumours (SFTs) are rare WHO grade I mesenchymal neoplasms that were first described in the visceral pleura. A wide variety of locations of SFT have been reported but only twelve cases of intramedullary solitary fibrous tumour. We report a case of thoracic spinal cord SFT.
A 49-year-old woman presented with clinical signs of dorsal myelopathy. Magnetic resonance imaging revealed an intradural mass at level T9–T10 which showed imaging features consistent both for an intra- and an extramedullary location of a solid tumour. Imaging findings were confirmed during surgery which was successful in resecting the extramedullary component. The intramedullary component could only be partially resected.
Solitary fibrous tumour is a rare pathological entity in the central nervous system. The course of intramedullary SFT is unknown and careful long-term follow-up is recommended.
Keywords
Solitary fibrous tumour, Intramedullary spinal cord tumour, Medullary tumour imaging, CD34, Bcl2
Title
Solitary fibrous tumour with intramedullary component: Case report and review of the literature
Journal
Neurologia i Neurochirurgia Polska
Issue
Pages
144-149
Page views
241
Article views/downloads
355
DOI
10.1016/j.pjnns.2013.09.006
Bibliographic record
Neurol Neurochir Pol 2014;48(2):144-149.
Keywords
Solitary fibrous tumour
Intramedullary spinal cord tumour
Medullary tumour imaging
CD34
Bcl2
Authors
Thomas Robert
Christophe Duc
Diego San Millán
Marc Morard