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Multiple spinal cavernous malformations in Klippel-Trenaunay-Weber syndrome
Affiliations- department of neurosurgery
- Autoimmune Blistering Dermatoses Section, Department of Dermatology, Poznan University of Medical Sciences, 49 Przybyszewskiego Street, 60-355 Poznan, Poland
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Abstract
Klippel-Trenaunay-Weber syndrome (KTWS) is a rare, congenital vascular disorder characterized by cutaneous haemangiomas, venous varicosities, and hypertrophy of the osseous and soft tissue. Various vascular anomalies of the central nervous system have been described in this syndrome. Two previous associations between KTWS and spinal cord cavernous malformations have been reported in the English literature. In this report, we present a patient in whom multiple cavernous malformations located in the conus medullaris region and cauda equina were associated with KTWS. General physical examination as well as neuroradiological and operative findings are described.
Abstract
Klippel-Trenaunay-Weber syndrome (KTWS) is a rare, congenital vascular disorder characterized by cutaneous haemangiomas, venous varicosities, and hypertrophy of the osseous and soft tissue. Various vascular anomalies of the central nervous system have been described in this syndrome. Two previous associations between KTWS and spinal cord cavernous malformations have been reported in the English literature. In this report, we present a patient in whom multiple cavernous malformations located in the conus medullaris region and cauda equina were associated with KTWS. General physical examination as well as neuroradiological and operative findings are described.
Keywords
spinal cord, cauda equina, cavernous malformation, Klippel-Trenaunay-Weber syndrome
About this articleTitle
Multiple spinal cavernous malformations in Klippel-Trenaunay-Weber syndrome
Journal
Neurologia i Neurochirurgia Polska
Issue
Pages
496-500
Page views
262
Article views/downloads
322
DOI
10.5114/ninp.2012.31362
Bibliographic record
Neurol Neurochir Pol 2012;46(5):496-500.
Keywords
spinal cord
cauda equina
cavernous malformation
Klippel-Trenaunay-Weber syndrome
Authors
Ethem Göksu
Erkan Alpsoy
Tanju Uçar
Recai Tuncer
