open access

Vol 13, No 3 (2020)
Guidelines / Expert consensus
Published online: 2020-12-03
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Emicizumab (Hemlibra®) u chorych na hemofilię A powikłaną inhibitorem czynnika VIII — wytyczne Grupy ds. Hemostazy Polskiego Towarzystwa Hematologów i Transfuzjologów

Jerzy Windyga, Krzysztof Chojnowski, Anna Klukowska, Paweł Łaguna, Magdalena Łętowska, Andrzej Mital, Wojciech Młynarski, Jacek Musiał, Jacek Treliński, Anetta Undas, Tomasz Urasiński, Joanna Zdziarska, Maria Podolak-Dawidziak
Journal of Transfusion Medicine 2020;13(3):153-164.

open access

Vol 13, No 3 (2020)
GUIDELINES
Published online: 2020-12-03

Abstract

W niniejszym artykule Grupa ds. Hemostazy Polskiego Towarzystwa Hematologów i Transfuzjologów przedstawiła zasady stosowania leku emicizumab. Emicizumab (Hemlibra ®, F. Hoffmann — La Roche, Bazylea, Szwajcaria) został dopuszczony do obrotu w krajach Unii Europejskiej w 2018 roku, a w Polsce jest dostępny dla chorych na hemofilię A powikłaną inhibitorem czynnika VIII od marca 2020 roku. Artykuł stanowi uzupełnienie wytycznych postępowania w hemofilii A i B powikłanej obecnością inhibitora czynnika VIII i IX, które ukazały się w 2017 roku.

Abstract

W niniejszym artykule Grupa ds. Hemostazy Polskiego Towarzystwa Hematologów i Transfuzjologów przedstawiła zasady stosowania leku emicizumab. Emicizumab (Hemlibra ®, F. Hoffmann — La Roche, Bazylea, Szwajcaria) został dopuszczony do obrotu w krajach Unii Europejskiej w 2018 roku, a w Polsce jest dostępny dla chorych na hemofilię A powikłaną inhibitorem czynnika VIII od marca 2020 roku. Artykuł stanowi uzupełnienie wytycznych postępowania w hemofilii A i B powikłanej obecnością inhibitora czynnika VIII i IX, które ukazały się w 2017 roku.

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Keywords

emicizumab; hemofilia A; inhibitor; profilaktyka; krwawienia; wytyczne; Polska; czynnik VIII; czynniki omijające; rVIIa; aPCC

About this article
Title

Emicizumab (Hemlibra®) u chorych na hemofilię A powikłaną inhibitorem czynnika VIII — wytyczne Grupy ds. Hemostazy Polskiego Towarzystwa Hematologów i Transfuzjologów

Journal

Journal of Transfusion Medicine

Issue

Vol 13, No 3 (2020)

Article type

Guidelines / Expert consensus

Pages

153-164

Published online

2020-12-03

Bibliographic record

Journal of Transfusion Medicine 2020;13(3):153-164.

Keywords

emicizumab
hemofilia A
inhibitor
profilaktyka
krwawienia
wytyczne
Polska
czynnik VIII
czynniki omijające
rVIIa
aPCC

Authors

Jerzy Windyga
Krzysztof Chojnowski
Anna Klukowska
Paweł Łaguna
Magdalena Łętowska
Andrzej Mital
Wojciech Młynarski
Jacek Musiał
Jacek Treliński
Anetta Undas
Tomasz Urasiński
Joanna Zdziarska
Maria Podolak-Dawidziak

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