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Vol 13, No 3 (2020)
Guidelines / Expert consensus
Published online: 2020-12-03

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Emicizumab (Hemlibra®) u chorych na hemofilię A powikłaną inhibitorem czynnika VIII — wytyczne Grupy ds. Hemostazy Polskiego Towarzystwa Hematologów i Transfuzjologów

Jerzy Windyga1, Krzysztof Chojnowski2, Anna Klukowska3, Paweł Łaguna3, Magdalena Łętowska4, Andrzej Mital5, Wojciech Młynarski6, Jacek Musiał7, Jacek Treliński8, Anetta Undas9, Tomasz Urasiński10, Joanna Zdziarska11, Maria Podolak-Dawidziak12
Journal of Transfusion Medicine 2020;13(3):153-164.

Abstract

W niniejszym artykule Grupa ds. Hemostazy Polskiego Towarzystwa Hematologów i Transfuzjologów przedstawiła zasady stosowania leku emicizumab. Emicizumab (Hemlibra ®, F. Hoffmann — La Roche, Bazylea, Szwajcaria) został dopuszczony do obrotu w krajach Unii Europejskiej w 2018 roku, a w Polsce jest dostępny dla chorych na hemofilię A powikłaną inhibitorem czynnika VIII od marca 2020 roku. Artykuł stanowi uzupełnienie wytycznych postępowania w hemofilii A i B powikłanej obecnością inhibitora czynnika VIII i IX, które ukazały się w 2017 roku.

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