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Images In Cardiology
Published online: 2019-07-02
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Juvenile Takayasu arteritis presenting with Aortic dissection as initial presentation

Santosh Kumar Sinha, Puneet Aggarwal, Mahmodula Razi, Kumar Himanshu, Siddarth Samrat, Vinay Krishna
DOI: 10.5603/FC.a2019.0080

open access

Ahead of print
Images In Cardiology
Published online: 2019-07-02

Abstract

A 6-year-old girl who was diagnosed Takayasu arteritis, had presented low grade fever, loss of appetite and weight, and breathlessness for 6 weeks. Echocardiography showed global hypokinesia with severely depressed systolic function (EF-20%). Multidetector computed tomography scan (MDCT) of aorta showed mild diffuse narrowing of thoraco-abdominal segment with severe narrowing of distal abdominal segment in infra renal segment with spiral flap suggesting aortic dissection (DeBakey type II; Stanford type III). Patient succumbed to death because of progressive failure and ventricular tachycardia. Here, we report a case of juvenile Takayasu arteritis with aortic dissection as its initial presentation.

Abstract

A 6-year-old girl who was diagnosed Takayasu arteritis, had presented low grade fever, loss of appetite and weight, and breathlessness for 6 weeks. Echocardiography showed global hypokinesia with severely depressed systolic function (EF-20%). Multidetector computed tomography scan (MDCT) of aorta showed mild diffuse narrowing of thoraco-abdominal segment with severe narrowing of distal abdominal segment in infra renal segment with spiral flap suggesting aortic dissection (DeBakey type II; Stanford type III). Patient succumbed to death because of progressive failure and ventricular tachycardia. Here, we report a case of juvenile Takayasu arteritis with aortic dissection as its initial presentation.

Get Citation

Keywords

Juvenile Takayasu arteritis; Aortic dissection, Sudden death

About this article
Title

Juvenile Takayasu arteritis presenting with Aortic dissection as initial presentation

Journal

Folia Cardiologica

Issue

Ahead of print

Published online

2019-07-02

DOI

10.5603/FC.a2019.0080

Keywords

Juvenile Takayasu arteritis
Aortic dissection
Sudden death

Authors

Santosh Kumar Sinha
Puneet Aggarwal
Mahmodula Razi
Kumar Himanshu
Siddarth Samrat
Vinay Krishna

References (7)
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