open access

Vol 13, No 6 (2018)
Case Reports
Published online: 2018-09-19
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Unexplained heart failure in a 14-month baby

Santosh Kumar Sinha, Puneet Aggarwal, Lokendra Rekwal, Sunil Tripathi, Nishant Kumar Abhishekh
DOI: 10.5603/FC.a2018.0121
·
Folia Cardiologica 2018;13(6):559-560.

open access

Vol 13, No 6 (2018)
Case Reports
Published online: 2018-09-19

Abstract

Endocardial fibroelastosis is a cardiomyopathy rarely seen in the present age. Here, we report a case of 14-months-old baby who presented with failure to thrive, sweating while feeding, a dilated left ventricle, and left ventricular dysfunction. Chest x-ray revealed cardiomegaly with pulmonary venous hypertension. Electrocardiogram showed left ventricular hypertrophy with strain pattern. Echocardiogram revealed dilated left ventricle with severe systolic dysfunction which was labelled as endocardial fibroelastosis. As there were no associated lesions, it was labelled as primary endocardial fibroelastosis (pEFE). The baby was managed conservatively. Here, we would like to highlight the fact that primary endocardial fibroelastosis (pEFE) can masquerade as idiopathic dilated cardiomyopathy. Progressive ventricular dilation and ventricular dysfunction portends poor prognosis, though few of them may be managed with conservative treatment.

Abstract

Endocardial fibroelastosis is a cardiomyopathy rarely seen in the present age. Here, we report a case of 14-months-old baby who presented with failure to thrive, sweating while feeding, a dilated left ventricle, and left ventricular dysfunction. Chest x-ray revealed cardiomegaly with pulmonary venous hypertension. Electrocardiogram showed left ventricular hypertrophy with strain pattern. Echocardiogram revealed dilated left ventricle with severe systolic dysfunction which was labelled as endocardial fibroelastosis. As there were no associated lesions, it was labelled as primary endocardial fibroelastosis (pEFE). The baby was managed conservatively. Here, we would like to highlight the fact that primary endocardial fibroelastosis (pEFE) can masquerade as idiopathic dilated cardiomyopathy. Progressive ventricular dilation and ventricular dysfunction portends poor prognosis, though few of them may be managed with conservative treatment.
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Keywords

cardiomyopathy, primary endocardial fibroelastosis, systolic dysfunction, dilated cardiomyopath

About this article
Title

Unexplained heart failure in a 14-month baby

Journal

Folia Cardiologica

Issue

Vol 13, No 6 (2018)

Pages

559-560

Published online

2018-09-19

DOI

10.5603/FC.a2018.0121

Bibliographic record

Folia Cardiologica 2018;13(6):559-560.

Keywords

cardiomyopathy
primary endocardial fibroelastosis
systolic dysfunction
dilated cardiomyopath

Authors

Santosh Kumar Sinha
Puneet Aggarwal
Lokendra Rekwal
Sunil Tripathi
Nishant Kumar Abhishekh

References (12)
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