Vol 64, No 6 (2013)
Review paper
Published online: 2013-12-31

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Gastroduodenal neuroendocrine neoplasms including gastrinoma — management guidelines (recommended by the Polish Network of Neuroendocrine Tumours)

Grażyna Rydzewska, Andrzej Cichocki, Jarosław B. Ćwikła, Wanda Foltyn, Alicja Hubalewska-Dydejczyk, Grzegorz Kamiński, Anna Lewczuk, Anna Nasierowska-Guttmejer, Ewa Nowakowska-Duława, Joanna Pilch-Kowalczyk, Anna Sowa-Staszczak, Beata Kos-Kudła, Other participants of the Consensus Conference (affiliations at the end of the paper):, Elżbieta Andrysiak-Mamos, Tomasz Bednarczuk, Jolanta Blicharz-Dorniak, Marek Bolanowski, Jarosław Ćwikła, Andrzej Deptała, Daria Handkiewucz-Junak, Marek Hartleb, Michał Jarząb, Arkadiusz Jeziorski, Dariusz Kajdaniuk, Aldona Kowalska, Robert Król, Leszek Królicki, Jolanta Kunikowska, Katarzyna Kuśnierz, Paweł Lampe, Dariusz Lange, Magdalena Londzin-Olesik, Przemysław Majewski, Bogdan Marek, Gabriela Mełeń-Mucha, Andrzej Nowak, Waldemar Patkowski, Violetta Rosiek, Marek Ruchała, Sławomir Rudzki, Philippe Ruszniewski, Teresa Starzyńska, Katarzyna Steinhof-Radwańska, Janusz Strzelczyk, Wojciech Zajęcki, Piotr Zdunowski, Anna Zemczak
DOI: 10.5603/EP.2013.0030
Endokrynol Pol 2013;64(6):444-458.

Abstract

This paper presents the updated Polish Neuroendocrine Tumour Network expert panel recommendations on the management of neuroendocrine neoplasms (NENs) of the stomach and duodenum, including gastrinoma. The recommendations discuss the epidemiology, pathogenesis and clinical presentation of these tumours as well as their diagnosis, including biochemical, histopathological and localisation diagnosis. The principles of treatment are discussed, including endoscopic, surgical, pharmacological and radionuclide treatment. Finally, recommendations on patient monitoring are given. (Endokrynol Pol 2013; 64 (6): 444–458)