Vol 68, No 1 (2017)
Case report
Published online: 2017-03-01

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Bilateral primary pigmented nodular adrenal disease as a component of Carney syndrome — case report

Dorota Sikorska, Lucyna Bednarek-Papierska, Ewa Mojs, Ewa Makowska, Marek Ruchała, Włodzimierz Samborski
Pubmed: 28255981
Endokrynol Pol 2017;68(1):70-72.

Abstract

We report a case of a 20-year-old patient with Cushing’s syndrome as a component of Carney syndrome. Carney syndrome is an autosomal dominant disease with co-existing bilateral pigmented nodular adrenal disease, heart and skin myxoma, skin pigmentation, breast fibroadenoma, testicular and ovarian tumours, thyroid tumours, and pituitary adenomas. (Endokrynol Pol 2017; 68 (1): 70–72)

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