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Bilateral primary pigmented nodular adrenal disease as a component of Carney syndrome — case report
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Abstract
We report a case of a 20-year-old patient with Cushing’s syndrome as a component of Carney syndrome. Carney syndrome is an autosomal dominant disease with co-existing bilateral pigmented nodular adrenal disease, heart and skin myxoma, skin pigmentation, breast fibroadenoma, testicular and ovarian tumours, thyroid tumours, and pituitary adenomas. (Endokrynol Pol 2017; 68 (1): 70–72)
Abstract
We report a case of a 20-year-old patient with Cushing’s syndrome as a component of Carney syndrome. Carney syndrome is an autosomal dominant disease with co-existing bilateral pigmented nodular adrenal disease, heart and skin myxoma, skin pigmentation, breast fibroadenoma, testicular and ovarian tumours, thyroid tumours, and pituitary adenomas. (Endokrynol Pol 2017; 68 (1): 70–72)
Keywords
Carney syndrome; Cushing' s syndrome; primary pigmented nodular adrenal disease; adrenalectomy
About this articleTitle
Bilateral primary pigmented nodular adrenal disease as a component of Carney syndrome — case report
Journal
Issue
Article type
Case report
Pages
70-72
Published online
2017-03-01
Page views
1631
Article views/downloads
1951
DOI
10.5603/EP.2017.0008
Pubmed
Bibliographic record
Endokrynol Pol 2017;68(1):70-72.
Keywords
Carney syndrome
Cushing's syndrome
primary pigmented nodular adrenal disease
adrenalectomy
Authors
Dorota Sikorska
Lucyna Bednarek-Papierska
Ewa Mojs
Ewa Makowska
Marek Ruchała
Włodzimierz Samborski
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