Vol 62, No 3 (2011)
Case report
Published online: 2011-06-29
Primary pigmented nodular adrenocortical disease
Endokrynol Pol 2011;62(3):268-270.
Abstract
Primary pigmented nodular adrenocortical disease (PPNAD) is a rare adrenal tumour causing corticotrophin-independent Cushing’s
syndrome. It occurs mainly in children and young adults. The histological examination is characterised by small pigmented micronodules
on the adrenal cortex. The diagnosis is most often seen in patients with Carney Complex, but it can also occur in isolation. We report
a case of Carney Complex that was referred for adrenalectomy. The procedure was uneventful and the patient was well at discharge. The
adrenal pathology showed numerous black nodules measuring less than 2mm in diameter. This feature was pathognomonic of primary
pigmented nodular adrenocortical disease. (Pol J Endocrinol 2011; 62 (3): 268–270)
Keywords: PPNADCarney complexadrenal glandtumour
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