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Vol 24, No 1-2 (2022)
Case report
Published online: 2022-08-05

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An uncommon cause of well-known symptoms: acute abdomen in a 2-year-old boy with intestinal malrotation. Case report and literature review

Patrycja Sosnowska-Sienkiewicz1, Maria Mitkowska2, Jakub Langa2, Przemysław Mańkowski1
Chirurgia Polska 2022;24(1-2):22-25.


Midgut malrotation is the most frequent congenital defect of the small intestine. The clinical manifestation can vary from being asymptomatic to presenting acutely as volvulus with bilious vomiting.

Presented here is a case of a 32-months-old boy with abdominal pain and several emetic episodes before admission. The patient was diagnosed with ileus and needed emergency surgery which showed the presence of volvulus due to malrotation of the midgut. Extensive partial resections of the jejunum, ileum and colon beginning in the upper part of the rectum up to ascending colon were performed.

Intestinal malrotation is rarely a symptomatic abnormality, however, when it occurs severely it can result in life-threatening complications. Ultrasonography may be a helpful screening tool for early diagnosis, but it needs the experience of the doctor. Treating significant malrotation almost always requires surgery. The timing and urgency depend on the child’s condition.

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