Vol 71, No 4 (2013)
Case studies
Published online: 2013-04-18
Atrial mechanical and electrical dysfunction in patient with Emery-Dreifuss muscular dystrophy reason of change in electrotherapeutical approach: frequent result of rare disease
DOI: 10.5603/KP.2013.0071
Kardiol Pol 2013;71(4):406-409.
Abstract
We present a case of a 35 year-old male patient with Emery-Dreifuss muscular dystrophy diagnosed in the age of 12 who
was assigned to dual chamber pacing system due to bradycardia primarily recognised as sinus node insufficiency with the
atrio-ventricular nodal rhythm. During the procedure permanent electrical atrial stand-still without atrial capture were detected
and the mode of stimulation was change to VVIR.
was assigned to dual chamber pacing system due to bradycardia primarily recognised as sinus node insufficiency with the
atrio-ventricular nodal rhythm. During the procedure permanent electrical atrial stand-still without atrial capture were detected
and the mode of stimulation was change to VVIR.
Keywords: Emery-Dreifuss muscular dystrophypermanent pacingatrial stand-still
