Synovial sarcoma of the neck
Abstract
Soft-tissue sarcomas originate from the mesodermal tissue. They mainly locate within extremities (50% of cases), trunk (30%), head and neck (10%), and in the retroperitoneal space (10%). Sarcomas represent about 1% of all malignant tumours in adults. So far, causes of the soft-tissue sarcomas have not been well recognised. These neoplasms occur more frequently in persons with genetic diseases. Frequent prevalence of sarcomas is observed in subjects with Von Recklinghausen disease (neurofibromatosis), Gardner syndrome, Werner syndrome, tuberous sclerosis, and Li-Fraumeni syndrome (mutation p53). This paper presents the case of a 29-year-old patient with a large tumour of the neck and Von Recklinghausen disease, referred to the Department of Thoracic Surgery with the diagnosis of MPNST (malignant peripheral nerve sheath tumours).
Keywords: soft tissue sarcomasynovial sarcoma
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