open access

Vol 11, No 6 (2015)
Case report
Published online: 2016-03-08
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Synovial sarcoma of the neck

Mariusz Stefański, Paweł Rogoziński, Krzysztof Bruliński
Oncol Clin Pract 2015;11(6):317-321.

open access

Vol 11, No 6 (2015)
CASE REPORT
Published online: 2016-03-08

Abstract

Soft-tissue sarcomas originate from the mesodermal tissue. They mainly locate within extremities (50% of cases), trunk (30%), head and neck (10%), and in the retroperitoneal space (10%). Sarcomas represent about 1% of all malignant tumours in adults. So far, causes of the soft-tissue sarcomas have not been well recognised. These neoplasms occur more frequently in persons with genetic diseases. Frequent prevalence of sarcomas is observed in subjects with Von Recklinghausen disease (neurofibromatosis), Gardner syndrome, Werner syndrome, tuberous sclerosis, and Li-Fraumeni syndrome (mutation p53). This paper presents the case of a 29-year-old patient with a large tumour of the neck and Von Recklinghausen disease, referred to the Department of Thoracic Surgery with the diagnosis of MPNST (malignant peripheral nerve sheath tumours).

Abstract

Soft-tissue sarcomas originate from the mesodermal tissue. They mainly locate within extremities (50% of cases), trunk (30%), head and neck (10%), and in the retroperitoneal space (10%). Sarcomas represent about 1% of all malignant tumours in adults. So far, causes of the soft-tissue sarcomas have not been well recognised. These neoplasms occur more frequently in persons with genetic diseases. Frequent prevalence of sarcomas is observed in subjects with Von Recklinghausen disease (neurofibromatosis), Gardner syndrome, Werner syndrome, tuberous sclerosis, and Li-Fraumeni syndrome (mutation p53). This paper presents the case of a 29-year-old patient with a large tumour of the neck and Von Recklinghausen disease, referred to the Department of Thoracic Surgery with the diagnosis of MPNST (malignant peripheral nerve sheath tumours).

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Keywords

soft tissue sarcoma, synovial sarcoma

About this article
Title

Synovial sarcoma of the neck

Journal

Oncology in Clinical Practice

Issue

Vol 11, No 6 (2015)

Article type

Case report

Pages

317-321

Published online

2016-03-08

Bibliographic record

Oncol Clin Pract 2015;11(6):317-321.

Keywords

soft tissue sarcoma
synovial sarcoma

Authors

Mariusz Stefański
Paweł Rogoziński
Krzysztof Bruliński

References (14)
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