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A child with a central nervous system relapse of a facial embryonal rhabdomyosarcoma
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Abstract
Rhabdomyosarcoma (RMS) is the most common type of soft tissue sarcoma in children. There are two main types of RMS: embryonal and alveolar (having a worse prognosis). The treatment for childhood RMS is based on surgery, chemotherapy and radiation. In spite of very intensive therapy, 1/3 of patients suffer a relapse. The case report presents a child with facial embryonal RMS with an atypical central nervous system relapse; this, despite a comprehensive diagnostic process, was diagnosed during the autopsy.
Abstract
Rhabdomyosarcoma (RMS) is the most common type of soft tissue sarcoma in children. There are two main types of RMS: embryonal and alveolar (having a worse prognosis). The treatment for childhood RMS is based on surgery, chemotherapy and radiation. In spite of very intensive therapy, 1/3 of patients suffer a relapse. The case report presents a child with facial embryonal RMS with an atypical central nervous system relapse; this, despite a comprehensive diagnostic process, was diagnosed during the autopsy.
Keywords
sarcoma, relapse, aseptic meningitis, childhood, chemotherapy, magnetic resonance imaging
About this articleTitle
A child with a central nervous system relapse of a facial embryonal rhabdomyosarcoma
Journal
Nowotwory. Journal of Oncology
Issue
Article type
Case report
Pages
322-325
Published online
2016-12-23
Page views
767
Article views/downloads
1604
DOI
Bibliographic record
Nowotwory. Journal of Oncology 2016;66(4):322-325.
Keywords
sarcoma
relapse
aseptic meningitis
childhood
chemotherapy
magnetic resonance imaging
Authors
Agata Adamczewska
Julita Janura-Szymańska
Klaudia Kończak
Wiesław Smoczyk
Miłosz Jazdon
Katarzyna Derwich
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