Vol 66, No 4 (2016)
Case report
Published online: 2016-12-23
A child with a central nervous system relapse of a facial embryonal rhabdomyosarcoma
Nowotwory. Journal of Oncology 2016;66(4):322-325.
Abstract
Rhabdomyosarcoma (RMS) is the most common type of soft tissue sarcoma in children. There are two main types of RMS: embryonal and alveolar (having a worse prognosis). The treatment for childhood RMS is based on surgery, chemotherapy and radiation. In spite of very intensive therapy, 1/3 of patients suffer a relapse. The case report presents a child with facial embryonal RMS with an atypical central nervous system relapse; this, despite a comprehensive diagnostic process, was diagnosed during the autopsy.
Keywords: sarcomarelapseaseptic meningitischildhoodchemotherapymagnetic resonance imaging
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