Acquired von Willebrand syndrome associated with indolent systemic mastocytosis
open access
Abstract
Hereby we present case report of acquired von Willebrand syndrome (AVWS) in patient with indolent systemic mastocytosis (ISM). Systemic mastocytosis may be considered as a model disease for development of AVWS. Thereinafter, pathophysiology of the disease as well as diagnostic and therapeutic approach were extensively discussed.
Abstract
Hereby we present case report of acquired von Willebrand syndrome (AVWS) in patient with indolent systemic mastocytosis (ISM). Systemic mastocytosis may be considered as a model disease for development of AVWS. Thereinafter, pathophysiology of the disease as well as diagnostic and therapeutic approach were extensively discussed.
Keywords
acquired von Willebrand syndrome; systemic mastocytosis; hemorrhagic diathesis
About this articleTitle
Acquired von Willebrand syndrome associated with indolent systemic mastocytosis
Journal
Journal of Transfusion Medicine
Issue
Article type
Case report
Pages
151-152
DOI
10.5603/JTM.2020.0005
Bibliographic record
Journal of Transfusion Medicine 2020;13(2):151-152.
Keywords
acquired von Willebrand syndrome
systemic mastocytosis
hemorrhagic diathesis
Authors
Alan Majeranowski
Andrzej Mital
Janusz Zawilski
Michał Czarnogórski
Aleksandra Janowiak-Majeranowska