Vol 13, No 2 (2020)
Case report
Published online: 2020-10-05
Acquired von Willebrand syndrome associated with indolent systemic mastocytosis
Journal of Transfusion Medicine 2020;13(2):151-152.
Abstract
Hereby we present case report of acquired von Willebrand syndrome (AVWS) in patient with indolent systemic mastocytosis (ISM). Systemic mastocytosis may be considered as a model disease for development of AVWS. Thereinafter, pathophysiology of the disease as well as diagnostic and therapeutic approach were extensively discussed.
Keywords: acquired von Willebrand syndromesystemic mastocytosishemorrhagic diathesis