Vol 13, No 2 (2022)
Review paper
Published online: 2022-10-20
Diagnosis and treatment of immune thrombocytopenia in Poland
1, 1
Hematology in Clinical Practice 2022;13(2):49-54.
Abstract
Immune thrombocytopenia (ITP) is an acquired autoimmune disease characterized by an isolated platelet count of less than 100,000/μL caused by destruction and reduced production of platelets. Systemic steroid therapy is a mainstay of first-line treatment; however, additional treatment lines are usually necessary due to the very high recurrence rate after therapy completion and steroid resistance. Standard treatment options for steroid resistance or steroid dependence include splenectomy, rituximab or thrombopoietin receptor agonists.
The article presents current data on the diagnosics and therapy of ITP, considering the limited access to some forms of treatment in Poland.
Keywords: idiopathic thrombocytopenic purpurasteroid-resistantsteroid-dependentTPO-RAsplenectomyrituximab
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