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Congenital diaphragmatic hernia: pathogenesis, prenatal diagnosis and management — literature review
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Abstract
Congenital diaphragmatic hernia (CDH) is a developmental discontinuity of the diaphragm. It allows abdominal viscera to herniate into the chest and leads to lung hypoplasia. Congenital diaphragmatic hernia is one of the most severe birth defects, with extremely high neonatal mortality. This paper presents a review of the available literature on prenatal diagnosis, management and treatment options for CDH. In selected cases, a prenatal procedure to improve neonatal survival is possible. The authors of this manuscript believe their work might contribute to a better understanding of congenital diaphragmatic hernia and patient selection for the FETO (fetal endoscopic tracheal occlusion) surgery or expectant management.
Abstract
Congenital diaphragmatic hernia (CDH) is a developmental discontinuity of the diaphragm. It allows abdominal viscera to herniate into the chest and leads to lung hypoplasia. Congenital diaphragmatic hernia is one of the most severe birth defects, with extremely high neonatal mortality. This paper presents a review of the available literature on prenatal diagnosis, management and treatment options for CDH. In selected cases, a prenatal procedure to improve neonatal survival is possible. The authors of this manuscript believe their work might contribute to a better understanding of congenital diaphragmatic hernia and patient selection for the FETO (fetal endoscopic tracheal occlusion) surgery or expectant management.
Keywords
congenital diaphragmatic hernia, FETO procedure, tracheal balloon occlusion, lung hypoplasia
About this articleTitle
Congenital diaphragmatic hernia: pathogenesis, prenatal diagnosis and management — literature review
Journal
Issue
Article type
Review paper
Pages
24-30
Published online
2017-01-31
Page views
13303
Article views/downloads
14094
DOI
Pubmed
Bibliographic record
Ginekol Pol 2017;88(1):24-30.
Keywords
congenital diaphragmatic hernia
FETO procedure
tracheal balloon occlusion
lung hypoplasia
Authors
Przemysław Kosiński
Mirosław Wielgoś
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