open access

Vol 88, No 1 (2017)
Review paper
Published online: 2017-01-31
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Congenital diaphragmatic hernia: pathogenesis, prenatal diagnosis and management — literature review

Przemysław Kosiński, Mirosław Wielgoś
DOI: 10.5603/GP.a2017.0005
·
Pubmed: 28157247
·
Ginekol Pol 2017;88(1):24-30.

open access

Vol 88, No 1 (2017)
REVIEW PAPERS Obstetrics
Published online: 2017-01-31

Abstract

Congenital diaphragmatic hernia (CDH) is a developmental discontinuity of the diaphragm. It allows abdominal viscera to herniate into the chest and leads to lung hypoplasia. Congenital diaphragmatic hernia is one of the most severe birth defects, with extremely high neonatal mortality. This paper presents a review of the available literature on prenatal diagnosis, management and treatment options for CDH. In selected cases, a prenatal procedure to improve neonatal survival is possible. The authors of this manuscript believe their work might contribute to a better understanding of congenital diaphragmatic hernia and patient selection for the FETO (fetal endoscopic tracheal occlusion) surgery or expectant management.

Abstract

Congenital diaphragmatic hernia (CDH) is a developmental discontinuity of the diaphragm. It allows abdominal viscera to herniate into the chest and leads to lung hypoplasia. Congenital diaphragmatic hernia is one of the most severe birth defects, with extremely high neonatal mortality. This paper presents a review of the available literature on prenatal diagnosis, management and treatment options for CDH. In selected cases, a prenatal procedure to improve neonatal survival is possible. The authors of this manuscript believe their work might contribute to a better understanding of congenital diaphragmatic hernia and patient selection for the FETO (fetal endoscopic tracheal occlusion) surgery or expectant management.

Get Citation

Keywords

congenital diaphragmatic hernia, FETO procedure, tracheal balloon occlusion, lung hypoplasia

About this article
Title

Congenital diaphragmatic hernia: pathogenesis, prenatal diagnosis and management — literature review

Journal

Ginekologia Polska

Issue

Vol 88, No 1 (2017)

Article type

Review paper

Pages

24-30

Published online

2017-01-31

DOI

10.5603/GP.a2017.0005

Pubmed

28157247

Bibliographic record

Ginekol Pol 2017;88(1):24-30.

Keywords

congenital diaphragmatic hernia
FETO procedure
tracheal balloon occlusion
lung hypoplasia

Authors

Przemysław Kosiński
Mirosław Wielgoś

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