Vol 6, No 2 (2020)
Review paper
Published online: 2020-07-09
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Giant cell arteritis — clinical presentation, diagnosis and treatment

Magdalena Żychowska1
·
Forum Dermatologicum 2020;6(2):59-62.
Affiliations
  1. Department of Dermatology, Institute of Medical Sciences, Medical College of Rzeszow University

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Vol 6, No 2 (2020)
REVIEW ARTICLES
Published online: 2020-07-09

Abstract

A systemic vasculitis is a diverse group of disorders, in which the immune-mediated inflammatory process primarily affects the walls of blood vessels. Giant cell arteritis (GCA), classified according to the International Chapel Hill Consensus Conference (2012) in the group of large vessel vasculitis, is a condition of a not fully understood aetiology, which predominantly affects women over 50 years of age. The initial phase of the disease is characterized by unspecific general symptoms. The paper aims to highlight the dermatological manifestations of the condition. GCA should be suspected in patients with erythema and oedema of the skin above the temporal artery and macular/bullous eruption or hair loss in the temporal area. In GCA, scalp necrosis, sometimes extensive and bilateral, as well as glossitis with bullous eruption or necrosis, may also occur. Treatment with systemic corticosteroids (CS) should be started as soon as the suspicion of GCA is raised to avoid irreversible complications, including permanent blindness.

Abstract

A systemic vasculitis is a diverse group of disorders, in which the immune-mediated inflammatory process primarily affects the walls of blood vessels. Giant cell arteritis (GCA), classified according to the International Chapel Hill Consensus Conference (2012) in the group of large vessel vasculitis, is a condition of a not fully understood aetiology, which predominantly affects women over 50 years of age. The initial phase of the disease is characterized by unspecific general symptoms. The paper aims to highlight the dermatological manifestations of the condition. GCA should be suspected in patients with erythema and oedema of the skin above the temporal artery and macular/bullous eruption or hair loss in the temporal area. In GCA, scalp necrosis, sometimes extensive and bilateral, as well as glossitis with bullous eruption or necrosis, may also occur. Treatment with systemic corticosteroids (CS) should be started as soon as the suspicion of GCA is raised to avoid irreversible complications, including permanent blindness.

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Keywords

systemic vasculitis; giant cell arteritis; scalp necrosis

About this article
Title

Giant cell arteritis — clinical presentation, diagnosis and treatment

Journal

Forum Dermatologicum

Issue

Vol 6, No 2 (2020)

Article type

Review paper

Pages

59-62

Published online

2020-07-09

Page views

1620

Article views/downloads

38

DOI

10.5603/FD.a2020.0008

Bibliographic record

Forum Dermatologicum 2020;6(2):59-62.

Keywords

systemic vasculitis
giant cell arteritis
scalp necrosis

Authors

Magdalena Żychowska

References (18)
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