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Lichen myxedematosus accompanied by Sjögren syndrome
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Abstract
Lichen myxedematosus belongs to the group of disorders with the deposition of mucins in the skin. The disease may coexist with monoclonal gammapathy, e.g. myeloma multiplex or Waldenström macroglobulinemia. A case of a 77-year-old man with lichen myxedematosus and monoclonal gammapathy is presented. Treatment with cyclophosphamide followed by intravenous immunoglobulins was initiated, however, no significant improvement of the skin condition was observed. Currently, the patient is receiving talidomide. This case report indicates, that lichen myxedematosus still remains a challenge for physicians and causes both diagnostics and therapeutic dilemma.
Abstract
Lichen myxedematosus belongs to the group of disorders with the deposition of mucins in the skin. The disease may coexist with monoclonal gammapathy, e.g. myeloma multiplex or Waldenström macroglobulinemia. A case of a 77-year-old man with lichen myxedematosus and monoclonal gammapathy is presented. Treatment with cyclophosphamide followed by intravenous immunoglobulins was initiated, however, no significant improvement of the skin condition was observed. Currently, the patient is receiving talidomide. This case report indicates, that lichen myxedematosus still remains a challenge for physicians and causes both diagnostics and therapeutic dilemma.
Keywords
monoclonal gammapathy, mucinosis
About this articleTitle
Lichen myxedematosus accompanied by Sjögren syndrome
Journal
Issue
Article type
Case report
Pages
44-47
Published online
2016-05-09
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483
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4869
Bibliographic record
Forum Dermatologicum 2016;2(1):44-47.
Keywords
monoclonal gammapathy
mucinosis
Authors
Joanna Gruber
Karolina Mędrek
Katarzyna Gruber-Szydło
Tomasz Wróbel
Adam Reich
Joanna Maj
