IgA vasculitis in an adult patient
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Abstract
Henoch–Schönlein purpura (HSP) is a form of small-vessel vasculitis characterized by the deposition of immunoglobulin A (IgA) in vascular walls. It predominantly affects children, often following a respiratory tract infection, and is marked by a classic tetrad of symptoms: palpable purpura, arthritis, abdominal pain, and haematuria. Though typically a paediatric condition, HSP can also occur in adults, where it may present with similar but sometimes more severe manifestations.
This article presents a case of IgA vasculitis with renal involvement in an adult patient treated with dapsone. Henoch–Schönlein purpura in adults presents unique challenges and requires a comprehensive, interdisciplinary approach to management. The absence of standardized treatment guidelines for adults highlights the need for further research and development of clear protocols. Collaboration among specialists in dermatology, nephrology, and other relevant fields is essential for optimizing patient care and outcomes in managing this complex condition.
Keywords: vasculitispurpuraIgA vasculitisdapsoneIgA nephropathy
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