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Rare malformations associated with partial anomalous pulmonary venous return: a cadaveric case report
- Institute of Anatomy and Cell Biology, Paracelsus Medical University, Nuremberg, Germany
open access
Abstract
A unique partial anomalous pulmonary venous return in combination with other rare malformations such as annular pancreas and a persistent umbilical vein was discovered in a female Caucasian cadaver during an anatomical dissection at the Paracelsus Medical University in Nuremberg, Germany. The pulmonary anomaly comprised the aberrant left superior pulmonary vein connecting the superior lobe of the left lung with the left brachiocephalic vein resulting in a left to right shunt. An annular pancreas without any signs causing duodenal compression was additionally found. To complete the constellation of malformations, a persistent umbilical vein within the round ligament fissure of the liver was also observed, connecting to an inferior branch of the extrahepatic left ramus of the portal vein. This rare constellation of malformations has been illustrated and thoroughly discussed with the currently available literature to develop a hypothesis for the genetic and developmental background.
Abstract
A unique partial anomalous pulmonary venous return in combination with other rare malformations such as annular pancreas and a persistent umbilical vein was discovered in a female Caucasian cadaver during an anatomical dissection at the Paracelsus Medical University in Nuremberg, Germany. The pulmonary anomaly comprised the aberrant left superior pulmonary vein connecting the superior lobe of the left lung with the left brachiocephalic vein resulting in a left to right shunt. An annular pancreas without any signs causing duodenal compression was additionally found. To complete the constellation of malformations, a persistent umbilical vein within the round ligament fissure of the liver was also observed, connecting to an inferior branch of the extrahepatic left ramus of the portal vein. This rare constellation of malformations has been illustrated and thoroughly discussed with the currently available literature to develop a hypothesis for the genetic and developmental background.
Keywords
partial anomalous pulmonary venous return, patent umbilical vein, annular pancreas
Title
Rare malformations associated with partial anomalous pulmonary venous return: a cadaveric case report
Journal
Issue
Article type
Case report
Pages
526-531
Published online
2021-03-01
Page views
5187
Article views/downloads
1294
DOI
Pubmed
Bibliographic record
Folia Morphol 2022;81(2):526-531.
Keywords
partial anomalous pulmonary venous return
patent umbilical vein
annular pancreas
Authors
S. Silawal
T. Essing
C. Schaupp
G. Schulze-Tanzil
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