open access

Vol 81, No 2 (2022)
Case report
Submitted: 2021-01-13
Accepted: 2021-02-11
Published online: 2021-03-01
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Rare malformations associated with partial anomalous pulmonary venous return: a cadaveric case report

S. Silawal1, T. Essing1, C. Schaupp1, G. Schulze-Tanzil1
DOI: 10.5603/FM.a2021.0026
·
Pubmed: 33749806
·
Folia Morphol 2022;81(2):526-531.
Affiliations
  1. Institute of Anatomy and Cell Biology, Paracelsus Medical University, Nuremberg, Germany

open access

Vol 81, No 2 (2022)
CASE REPORTS
Submitted: 2021-01-13
Accepted: 2021-02-11
Published online: 2021-03-01

Abstract

A unique partial anomalous pulmonary venous return in combination with other rare malformations such as annular pancreas and a persistent umbilical vein was discovered in a female Caucasian cadaver during an anatomical dissection at the Paracelsus Medical University in Nuremberg, Germany. The pulmonary anomaly comprised the aberrant left superior pulmonary vein connecting the superior lobe of the left lung with the left brachiocephalic vein resulting in a left to right shunt. An annular pancreas without any signs causing duodenal compression was additionally found. To complete the constellation of malformations, a persistent umbilical vein within the round ligament fissure of the liver was also observed, connecting to an inferior branch of the extrahepatic left ramus of the portal vein. This rare constellation of malformations has been illustrated and thoroughly discussed with the currently available literature to develop a hypothesis for the genetic and developmental background.

Abstract

A unique partial anomalous pulmonary venous return in combination with other rare malformations such as annular pancreas and a persistent umbilical vein was discovered in a female Caucasian cadaver during an anatomical dissection at the Paracelsus Medical University in Nuremberg, Germany. The pulmonary anomaly comprised the aberrant left superior pulmonary vein connecting the superior lobe of the left lung with the left brachiocephalic vein resulting in a left to right shunt. An annular pancreas without any signs causing duodenal compression was additionally found. To complete the constellation of malformations, a persistent umbilical vein within the round ligament fissure of the liver was also observed, connecting to an inferior branch of the extrahepatic left ramus of the portal vein. This rare constellation of malformations has been illustrated and thoroughly discussed with the currently available literature to develop a hypothesis for the genetic and developmental background.

Get Citation

Keywords

partial anomalous pulmonary venous return, patent umbilical vein, annular pancreas

About this article
Title

Rare malformations associated with partial anomalous pulmonary venous return: a cadaveric case report

Journal

Folia Morphologica

Issue

Vol 81, No 2 (2022)

Article type

Case report

Pages

526-531

Published online

2021-03-01

Page views

1286

Article views/downloads

644

DOI

10.5603/FM.a2021.0026

Pubmed

33749806

Bibliographic record

Folia Morphol 2022;81(2):526-531.

Keywords

partial anomalous pulmonary venous return
patent umbilical vein
annular pancreas

Authors

S. Silawal
T. Essing
C. Schaupp
G. Schulze-Tanzil

References (24)
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