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A rare cause of congenital portosystemic shunt: type 2 Abernethy malformation
, 2, 1, 3
Affiliations- Department of Radiology, Medical Faculty, Ataturk University, Erzurum, Türkiye
- Mus State Hospital, Mus, Türkiye
- Department of Radiology, Medical Faculty, Ataturk University, Erzurum, Turkey
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Abstract
The Abernethy malformation is characterised by congenital extrahepatic portosystemic shunts and is divided into two groups according to the type of anastomosis. In type 1, all portal venous blood is discharged into the inferior vena cava and there is no intrahepatic portal vein. In type 2, the portal vein is partially discharged to the inferior vena cava via side-by-side anastomoses. Imaging has an important role in the diagnosis and follow-up of this malformation. Magnetic resonance imaging should be preferred to demonstrate both vessel anatomy and associated anomalies. The aim of this study was to present a 17-year-old male patient and to discuss the imaging findings of Abernethy malformation.
Abstract
The Abernethy malformation is characterised by congenital extrahepatic portosystemic shunts and is divided into two groups according to the type of anastomosis. In type 1, all portal venous blood is discharged into the inferior vena cava and there is no intrahepatic portal vein. In type 2, the portal vein is partially discharged to the inferior vena cava via side-by-side anastomoses. Imaging has an important role in the diagnosis and follow-up of this malformation. Magnetic resonance imaging should be preferred to demonstrate both vessel anatomy and associated anomalies. The aim of this study was to present a 17-year-old male patient and to discuss the imaging findings of Abernethy malformation.
Keywords
Abernethy malformation, magnetic resonance imaging, radiology
About this articleTitle
A rare cause of congenital portosystemic shunt: type 2 Abernethy malformation
Journal
Issue
Article type
Case report
Pages
172-175
Published online
2019-05-20
Page views
3011
Article views/downloads
772
DOI
Pubmed
Bibliographic record
Folia Morphol 2020;79(1):172-175.
Keywords
Abernethy malformation
magnetic resonance imaging
radiology
Authors
O. Taydas
G. Danisan
H. Ogul
M. Kantarci
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