Vol 79, No 4 (2020)
Case report
Published online: 2020-01-07
Duplication of the spleen accompanied by multiple anomalies of the thorax and abdomen: a rare case
Abstract
Duplication of the spleen, classified as a polysplenia syndrome, is a very rare anomaly. Polysplenia is a complex syndrome with a broad spectrum of abnormalities. Other abnormalities accompanying polysplenia have been previously reported. In this paper, we present a case of duplication of the spleen accompanied by multiple anomalies in the thorax and abdomen.
Keywords: spleenduplicationcomputed tomography
References
- Applegate KE, Goske MJ, Pierce G, et al. Situs revisited: imaging of the heterotaxy syndrome. Radiographics. 1999; 19(4): 837–52; discussion 853.
- Duarte R, Morais H. Aortic pseudocoarctation associated with polysplenia/heterotaxy syndrome. Rev Port Cardiol. 2015; 34(1): 73.e1–73.e3.
- Fulcher AS, Turner MA. Abdominal manifestations of situs anomalies in adults. Radiographics. 2002; 22(6): 1439–1456.
- Griffiths JD, Marshall VC. Torsion of the spleen in the polysplenia syndrome. Aust N Z J Surg. 1984; 54(6): 571–573.
- Herman TE, Siegel MJ. Polysplenia syndrome with congenital short pancreas. AJR Am J Roentgenol. 1991; 156(4): 799–800.
- Kandpal H, Sharma R, Gamangatti S, et al. Imaging the inferior vena cava: a road less traveled. Radiographics. 2008; 28(3): 669–689.
- Kim SW, Shin HC, Kim IY, et al. Duplication of the spleen with a short pancreas. Br J Radiol. 2009; 82(975): e42–e43.
- Low JP, Williams D, Chaganti JR. Polysplenia syndrome with agenesis of the dorsal pancreas and preduodenal portal vein presenting with obstructive jaundice: a case report and literature review. Br J Radiol. 2011; 84(1007): e217–e220.
- Paramasivam V, Anand A, Shastri D, et al. Duplication Of Spleen A Rare Case Report. NJBMS. 2014; 4.
- Peoples WM, Moller JH, Edwards JE. Polysplenia: a review of 146 cases. Pediatr Cardiol. 1983; 4(2): 129–137.
- Rameshbabu CS, Gupta KK, Qasim M, et al. Heterotaxy polysplenia syndrome in an adult with unique vascular anomalies: case report with review of literature. J Radiol Case Rep. 2015; 9(7): 22–37.
- Sener RN, Alper H. Polysplenia syndrome: a case associated with transhepatic portal vein, short pancreas, and left inferior vena cava with hemiazygous continuation. Abdom Imaging. 1994; 19(1): 64–66.
- Sharma P, Alkadhi H, Gubler C, et al. Splenic duplication: a rare cause of acute upper gastrointestinal bleeding. Abdom Imaging. 2013; 38(1): 163–166.
- Tawfik AM, Batouty NM, Zaky MM, et al. Polysplenia syndrome: a review of the relationship with viscero-atrial situs and the spectrum of extra-cardiac anomalies. Surg Radiol Anat. 2013; 35(8): 647–653.
- Wainwright H, Nelson M. Polysplenia syndrome and congenital short pancreas. Am J Med Genet. 1993; 47(3): 318–320.
- Wolla CD, Hlavacek AM, Schoepf UJ, et al. Cardiovascular manifestations of heterotaxy and related situs abnormalities assessed with CT angiography. J Cardiovasc Comput Tomogr. 2013; 7(6): 408–416.