open access

Vol 79, No 1 (2020)
CASE REPORTS
Published online: 2019-05-20
Submitted: 2019-04-07
Accepted: 2019-05-08
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A rare cause of congenital portosystemic shunt: type 2 Abernethy malformation

O. Taydas, G. Danisan, H. Ogul, M. Kantarci
DOI: 10.5603/FM.a2019.0063
·
Pubmed: 31282554
·
Folia Morphol 2020;79(1):172-175.

open access

Vol 79, No 1 (2020)
CASE REPORTS
Published online: 2019-05-20
Submitted: 2019-04-07
Accepted: 2019-05-08

Abstract

The Abernethy malformation is characterised by congenital extrahepatic portosystemic shunts and is divided into two groups according to the type of anastomosis. In type 1, all portal venous blood is discharged into the inferior vena cava and there is no intrahepatic portal vein. In type 2, the portal vein is partially discharged to the inferior vena cava via side-by-side anastomoses. Imaging has an important role in the diagnosis and follow-up of this malformation. Magnetic resonance imaging should be preferred to demonstrate both vessel anatomy and associated anomalies. The aim of this study was to present a 17-year-old male patient and to discuss the imaging findings of Abernethy malformation.

Abstract

The Abernethy malformation is characterised by congenital extrahepatic portosystemic shunts and is divided into two groups according to the type of anastomosis. In type 1, all portal venous blood is discharged into the inferior vena cava and there is no intrahepatic portal vein. In type 2, the portal vein is partially discharged to the inferior vena cava via side-by-side anastomoses. Imaging has an important role in the diagnosis and follow-up of this malformation. Magnetic resonance imaging should be preferred to demonstrate both vessel anatomy and associated anomalies. The aim of this study was to present a 17-year-old male patient and to discuss the imaging findings of Abernethy malformation.

Get Citation

Keywords

Abernethy malformation, magnetic resonance imaging, radiology

About this article
Title

A rare cause of congenital portosystemic shunt: type 2 Abernethy malformation

Journal

Folia Morphologica

Issue

Vol 79, No 1 (2020)

Pages

172-175

Published online

2019-05-20

DOI

10.5603/FM.a2019.0063

Pubmed

31282554

Bibliographic record

Folia Morphol 2020;79(1):172-175.

Keywords

Abernethy malformation
magnetic resonance imaging
radiology

Authors

O. Taydas
G. Danisan
H. Ogul
M. Kantarci

References (19)
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