Left ventricular non-compaction cardiomyopathy: a rare cause of cardiovascular complaints
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Streszczenie
20-year-old woman with diagnosed in childhood left ventricular non-compaction (LVNC) cardiomyopathy with coexisting arthrogryposis was admitted to the Department of Cardiology due to atypical chest pain, worsening of exercise tolerance, bendopnea and symptoms of bronchial asthma exacerbation. The electrocardiogram (ECG) showed changes indicative of ischemia, without their dynamics. Inflammatory parameters, BNP (B-type natriuretic peptide), and myocardial necrosis markers were not elevated. Systolic and diastolic function on echocardiography (ECHO) was assessed as normal. Despite the initially suggestive clinical picture, the correct direction of the differential diagnosis, and consequently the diagnosis, was established after completing the history of comorbidities.
Słowa kluczowe: LVNCcardiomyopathyarthrogryposis
Referencje
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