Vol 14, No 4 (2019)
Case report
Published online: 2019-07-02
Pulmonary hypertension of complex aetiology: contemporary treatment options
Folia Cardiologica 2019;14(4):397-400.
Abstract
We present the case of an 80 year-old female patient with pulmonary arterial hypertension of complex aetiology,
including late-diagnosed congenital heart disease. We describe the diagnostic procedures and staged treatment (percutaneous
closure of an ostium secundum atrial septal defect and drug treatment with riociguat) which resulted in
a significant clinical improvement.
Keywords: pulmonary hypertensionatrial septal defectchronic thromboembolic pulmonary hypertensionriociguat
References
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- Ghofrani HA, D'Armini AM, Grimminger F, et al. CHEST-1 Study Group. Riociguat for the treatment of chronic thromboembolic pulmonary hypertension. N Engl J Med. 2013; 369(4): 319–329.
- Galiè N, Grimminger F, Grünig E, et al. PATENT-1 Study Group. Riociguat for the treatment of pulmonary arterial hypertension. N Engl J Med. 2013; 369(4): 330–340.
