open access

Vol 13, No 4 (2018)
Cardiology Investigation
Published online: 2018-09-12
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Non-compaction cardiomyopathy

Natalia Pietraszek, Dorota Piotrowska-Kownacka, Renata Główczyńska
DOI: 10.5603/FC.2018.0081
·
Pubmed: 22591194
·
Folia Cardiologica 2018;13(4):378-385.

open access

Vol 13, No 4 (2018)
Cardiology Investigation
Published online: 2018-09-12

Abstract

Non-compaction cardiomyopathy is a rare genetic condition and may occur either in a familial form or in a sporadic form. It is characterized by excessive trabeculation and occurrence of deep intertrabecular recesses. Usually the diagnosis is made during an accidental echocardiography or during the screening process of the family members. Although there is no gold standard for the diagnosis, Jenni et al. criteria used during echocardiography examination are the most common. Treatment is based on suppressing the progression of heart failure, thromboembolism prevention and dealing with arrhythmias. Moreover, patients have often cardioverter-defibrillator implanted and they are enrolled on the heart transplant list.

Abstract

Non-compaction cardiomyopathy is a rare genetic condition and may occur either in a familial form or in a sporadic form. It is characterized by excessive trabeculation and occurrence of deep intertrabecular recesses. Usually the diagnosis is made during an accidental echocardiography or during the screening process of the family members. Although there is no gold standard for the diagnosis, Jenni et al. criteria used during echocardiography examination are the most common. Treatment is based on suppressing the progression of heart failure, thromboembolism prevention and dealing with arrhythmias. Moreover, patients have often cardioverter-defibrillator implanted and they are enrolled on the heart transplant list.
Get Citation

Keywords

non-compaction cardiomyopathy, heart failure, echocardiography, magnetic resonance

About this article
Title

Non-compaction cardiomyopathy

Journal

Folia Cardiologica

Issue

Vol 13, No 4 (2018)

Pages

378-385

Published online

2018-09-12

DOI

10.5603/FC.2018.0081

Pubmed

22591194

Bibliographic record

Folia Cardiologica 2018;13(4):378-385.

Keywords

non-compaction cardiomyopathy
heart failure
echocardiography
magnetic resonance

Authors

Natalia Pietraszek
Dorota Piotrowska-Kownacka
Renata Główczyńska

References (22)
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