Vol 13, No 6 (2018)
Case report
Published online: 2018-09-19
Chronic reversible post-rheumatic fever: Jaccoud’s arthropathy in a 21 year-old male
DOI: 10.5603/FC.a2018.0105
Folia Cardiologica 2018;13(6):561-564.
Abstract
Jaccoud’s arthropathy (JA) is a condition characterised clinically by ‘reversible’ joint deformities resulting from soft tissue
abnormalities, rather than the destruction of bone joints. Although rare, it has been described in patients with chronic
rheumatic heart disease. It typically involves metacarpophalangeal and metatarsophalangeal joints. JA has also been
described in systemic lupus erythematosus (SLE), infections and neoplasia. Here, we report the case of a 21 year-old
male who had presented with a 16-year history of polyarthralgia, deformities of the hands for the last four years, and
a three-year history of exertional palpitation and dyspnoea. Physical examination revealed peripheral signs of aortic
run off, with hyperdynamic left ventricle and chronic severe aortic and mitral regurgitation. On examination, gross deformities
were noted in both hands in the form of ulnar deviation, swan neck, and ‘z’-thumb, involving interphalangeal
joints, metacarpophalangeal and first carpometacarpal joints which were partially correctable. Laboratory investigations
ruled out rheumatoid arthritis, SLE, and acute rheumatic fever. Chest X-ray, electrocardiogram and two-dimensional
echocardiography and Doppler study were consistent with chronic severe aortic regurgitation and severe mitral regurgitation.
Radiographs of both hands showed posterior subluxation of the carpometacarpal joints, which were completely
correctable. JA involving a carpometacarpal joint is exceedingly rare.
Keywords: Jaccoud’s arthropathyrheumatic heart diseasemetacarpophalangeal jointscarpometacarpal jointsswan neck deformity
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