Vol 72, No 4 (2021)
Clinical vignette
Published online: 2021-05-17

open access

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Clinical challenges and dilemmas in the management of advanced pancreatic neuroendocrine tumour — the first manifestation of von Hippel-Lindau disease in a young patient

Karolina Morawiec-Sławek1, Marta Opalińska2, Agnieszka Stefańska2, Anna Sowa-Staszczak1, Alicja Hubalewska-Dydejczyk1
Pubmed: 34010452
Endokrynol Pol 2021;72(4):412-413.


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  2. Krauss T, Ferrara AM, Links TP, et al. Preventive medicine of von Hippel-Lindau disease-associated pancreatic neuroendocrine tumors. Endocr Relat Cancer. 2018; 25(9): 783–793.
  3. Falconi M, Eriksson B, Kaltsas G, et al. Vienna Consensus Conference participants. ENETS Consensus Guidelines Update for the Management of Patients with Functional Pancreatic Neuroendocrine Tumors and Non-Functional Pancreatic Neuroendocrine Tumors. Neuroendocrinology. 2016; 103(2): 153–171.
  4. Ahmad S, Naber MR, Giles RH, et al. Diagnostic and management strategies for pNETs in Von Hippel-Lindau: a systematic review. Endocr Relat Cancer. 2021; 28(3): 151–160.
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