Upper extremity critical ischaemia in the course of sticky platelet syndrome
, 2, 1, 3, 4, 3
Abstract
Introduction: Sticky platelet syndrome (SPS) is known as a rare thrombocytopathy with a genetic basis that can lead to the development of arterial or rarely venous thrombosis. The article presents the case of a 38-year-old woman with no history of thrombosis with symptoms of acute left upper limb ischaemia.
Case report: During hospitalisation, the patient underwent twice targeted thrombolysis of the left upper limb and mechanical thrombectomy of the left upper limb arteries with simultaneous percutaneous angioplasty, with minimal clinical improvement. Despite the treatment implemented, the progression of ischaemic changes in the limb was observed. To date, very few cases of peripheral ischaemia in SPS have been described. Aware of the challenge of making a correct diagnosis, as well as the subsequent care of a general practitioner (GP) for a patient with such a rare syndrome — the authors describe the case of a patient who developed a manifestation of SPS and received non-standard alprostadil therapy.
Keywords: critical limb ischaemiasticky platelet syndromethrombocytopathyupper limb necrosisalprostadil
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