open access

Vol 52, No 1 (2018)
Case reports
Submitted: 2017-08-02
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Posterior reversible encephalopathy syndrome in IgA vasculitis: Neuroimaging of a 14-year-old child

Harun Arslan, Alpaslan Yavuz, Ayşe Arslan, Abdurrahman Aycan
DOI: 10.1016/j.pjnns.2017.11.006
·
Neurol Neurochir Pol 2018;52(1):107-111.

open access

Vol 52, No 1 (2018)
Case reports
Submitted: 2017-08-02

Abstract

IgA vasculitis (IgAV) is a leukocytoclastic vasculitis and characterized by involvement of small vessels in skin, gastrointestinal system, joints, kidneys, and less frequently other organs. It is the commonest vasculitis in childhood and etiology is not completely known. Neurological manifestations of IgAV are very rare and usually seen in patients with severe hypertension or as an uncommon feature such as peripheral neuropathy. Posterior reversible encephalopathy syndrome (PRES) is a clinic-radiologic entity characterized with temporary vasogenic edema developing typically in posterior circulation of the brain and has been reported as a rare manifestation of IgAV. In this paper, a PRES case of 14-year-old male with IgAV is reported and etiopathogenesis was discussed with literature. Diagnosis was made by magnetic resonance imaging because of the existence of neurological symptoms (headache and visual loss) during the course of disease. His radiological findings have resolved with therapy. Although neurological involvement is a rare manifestation in IgAV, we recommend magnetic resonance imaging in such patients for diagnosis and evaluation of complications.

Abstract

IgA vasculitis (IgAV) is a leukocytoclastic vasculitis and characterized by involvement of small vessels in skin, gastrointestinal system, joints, kidneys, and less frequently other organs. It is the commonest vasculitis in childhood and etiology is not completely known. Neurological manifestations of IgAV are very rare and usually seen in patients with severe hypertension or as an uncommon feature such as peripheral neuropathy. Posterior reversible encephalopathy syndrome (PRES) is a clinic-radiologic entity characterized with temporary vasogenic edema developing typically in posterior circulation of the brain and has been reported as a rare manifestation of IgAV. In this paper, a PRES case of 14-year-old male with IgAV is reported and etiopathogenesis was discussed with literature. Diagnosis was made by magnetic resonance imaging because of the existence of neurological symptoms (headache and visual loss) during the course of disease. His radiological findings have resolved with therapy. Although neurological involvement is a rare manifestation in IgAV, we recommend magnetic resonance imaging in such patients for diagnosis and evaluation of complications.

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Keywords

Posterior leukoencephalopathy syndrome, IgA vasculitis, Children, Hypertension, Nephritis

About this article
Title

Posterior reversible encephalopathy syndrome in IgA vasculitis: Neuroimaging of a 14-year-old child

Journal

Neurologia i Neurochirurgia Polska

Issue

Vol 52, No 1 (2018)

Pages

107-111

DOI

10.1016/j.pjnns.2017.11.006

Bibliographic record

Neurol Neurochir Pol 2018;52(1):107-111.

Keywords

Posterior leukoencephalopathy syndrome
IgA vasculitis
Children
Hypertension
Nephritis

Authors

Harun Arslan
Alpaslan Yavuz
Ayşe Arslan
Abdurrahman Aycan

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