open access
Posterior reversible encephalopathy syndrome in IgA vasculitis: Neuroimaging of a 14-year-old child
Affiliations- Department of Radiology, Van Yuzuncu Yıl University, Dursun Odabası Faculty of Medicine, Van, Türkiye
- Department of Nutrition, Faculty of Health Science, Van Yuzuncu Yıl University, Van, Türkiye
- Department of Brain Surgery, Van Yuzuncu Yıl University, Dursun Odabası Faculty of Medicine, Van, Türkiye
open access
Abstract
IgA vasculitis (IgAV) is a leukocytoclastic vasculitis and characterized by involvement of small vessels in skin, gastrointestinal system, joints, kidneys, and less frequently other organs. It is the commonest vasculitis in childhood and etiology is not completely known. Neurological manifestations of IgAV are very rare and usually seen in patients with severe hypertension or as an uncommon feature such as peripheral neuropathy. Posterior reversible encephalopathy syndrome (PRES) is a clinic-radiologic entity characterized with temporary vasogenic edema developing typically in posterior circulation of the brain and has been reported as a rare manifestation of IgAV. In this paper, a PRES case of 14-year-old male with IgAV is reported and etiopathogenesis was discussed with literature. Diagnosis was made by magnetic resonance imaging because of the existence of neurological symptoms (headache and visual loss) during the course of disease. His radiological findings have resolved with therapy. Although neurological involvement is a rare manifestation in IgAV, we recommend magnetic resonance imaging in such patients for diagnosis and evaluation of complications.
Abstract
IgA vasculitis (IgAV) is a leukocytoclastic vasculitis and characterized by involvement of small vessels in skin, gastrointestinal system, joints, kidneys, and less frequently other organs. It is the commonest vasculitis in childhood and etiology is not completely known. Neurological manifestations of IgAV are very rare and usually seen in patients with severe hypertension or as an uncommon feature such as peripheral neuropathy. Posterior reversible encephalopathy syndrome (PRES) is a clinic-radiologic entity characterized with temporary vasogenic edema developing typically in posterior circulation of the brain and has been reported as a rare manifestation of IgAV. In this paper, a PRES case of 14-year-old male with IgAV is reported and etiopathogenesis was discussed with literature. Diagnosis was made by magnetic resonance imaging because of the existence of neurological symptoms (headache and visual loss) during the course of disease. His radiological findings have resolved with therapy. Although neurological involvement is a rare manifestation in IgAV, we recommend magnetic resonance imaging in such patients for diagnosis and evaluation of complications.
Keywords
Posterior leukoencephalopathy syndrome, IgA vasculitis, Children, Hypertension, Nephritis
About this articleTitle
Posterior reversible encephalopathy syndrome in IgA vasculitis: Neuroimaging of a 14-year-old child
Journal
Neurologia i Neurochirurgia Polska
Issue
Pages
107-111
Published online
2017-11-14
Page views
359
Article views/downloads
709
DOI
10.1016/j.pjnns.2017.11.006
Bibliographic record
Neurol Neurochir Pol 2018;52(1):107-111.
Keywords
Posterior leukoencephalopathy syndrome
IgA vasculitis
Children
Hypertension
Nephritis
Authors
Harun Arslan
Alpaslan Yavuz
Ayşe Arslan
Abdurrahman Aycan
