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Clinical vignette
Published online: 2023-01-10
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Successful treatment of pulmonary hypertension with macitentan in a patient with Hermansky-Pudlak syndrome

Akin Torun1, Almina Erdem1, Mustafa Oguz1, Tufan Cinar1
DOI: 10.33963/KP.a2023.0012
·
Pubmed: 36640015
Affiliations
  1. Health Sciences University, Sultan II. Abdülhamid Han Training and Research Hospital, Department of Cardiology, Tibbiye Street, Uskudar, Istanbul, Turkey

open access

Online first
Clinical vignette
Published online: 2023-01-10

Abstract

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Abstract

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Get Citation
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About this article
Title

Successful treatment of pulmonary hypertension with macitentan in a patient with Hermansky-Pudlak syndrome

Journal

Kardiologia Polska (Polish Heart Journal)

Issue

Online first

Article type

Clinical vignette

Published online

2023-01-10

Page views

72

Article views/downloads

42

DOI

10.33963/KP.a2023.0012

Pubmed

36640015

Authors

Akin Torun
Almina Erdem
Mustafa Oguz
Tufan Cinar

References (5)
  1. Vicary GW, Vergne Y, Santiago-Cornier A, et al. Pulmonary fibrosis in Hermansky-Pudlak syndrome. Ann Am Thorac Soc. 2016; 13(10): 1839–1846.
  2. El-Chemaly S, Young LR. Hermansky-Pudlak syndrome. Clin Chest Med. 2016; 37(3): 505–511.
  3. Lareo A, Nuche J, Cristo Ropero MJ, et al. Recent advances in the pharmacotherapy of pulmonary hypertension: practical considerations. Kardiol Pol. 2021; 79(4): 386–392.
  4. Pieniak K, Gąsecka A, Pietrasik A, et al. Diagnostic challenges to determine the cause of pulmonary hypertension in a patient with heart failure with preserved ejection fraction and borderline pulmonary artery wedge pressure. Kardiol Pol. 2022; 80(2): 222–223.
  5. Humbert M, Kovacs G, Hoeper MM, et al. 2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Heart J. 2022; 43(38): 3618–3731.

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