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Successful treatment of pulmonary hypertension with macitentan in a patient with Hermansky-Pudlak syndrome
Affiliations- Health Sciences University, Sultan II. Abdülhamid Han Training and Research Hospital, Department of Cardiology, Tibbiye Street, Uskudar, Istanbul, Turkey
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Abstract
Abstract
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About this articleTitle
Successful treatment of pulmonary hypertension with macitentan in a patient with Hermansky-Pudlak syndrome
Journal
Kardiologia Polska (Polish Heart Journal)
Issue
Article type
Clinical vignette
Published online
2023-01-10
Page views
72
Article views/downloads
42
DOI
10.33963/KP.a2023.0012
Pubmed
Authors
Akin Torun
Almina Erdem
Mustafa Oguz
Tufan Cinar
References (5)- Vicary GW, Vergne Y, Santiago-Cornier A, et al. Pulmonary fibrosis in Hermansky-Pudlak syndrome. Ann Am Thorac Soc. 2016; 13(10): 1839–1846.
- El-Chemaly S, Young LR. Hermansky-Pudlak syndrome. Clin Chest Med. 2016; 37(3): 505–511.
- Lareo A, Nuche J, Cristo Ropero MJ, et al. Recent advances in the pharmacotherapy of pulmonary hypertension: practical considerations. Kardiol Pol. 2021; 79(4): 386–392.
- Pieniak K, Gąsecka A, Pietrasik A, et al. Diagnostic challenges to determine the cause of pulmonary hypertension in a patient with heart failure with preserved ejection fraction and borderline pulmonary artery wedge pressure. Kardiol Pol. 2022; 80(2): 222–223.
- Humbert M, Kovacs G, Hoeper MM, et al. 2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Heart J. 2022; 43(38): 3618–3731.
