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open access

Vol 80, No 11 (2022)
Expert opinion
Published online: 2022-11-30
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Lung transplantation in patients with pulmonary arterial hypertension: The opinion of the Polish Cardiac Society Working Group on Pulmonary Circulation

Tatiana Mularek-Kubzdela1, Jacek Wojnarski2, Karol Kamiński34, Marek Ochman56, Jarosław D Kasprzak7, Tomasz Stącel56, Marcin Kurzyna8, Wojciech Karolak2, Ewa Mroczek9, Grzegorz Kopeć1011, Roman Przybylski12, Ilona Skorzylas13, Sławomir Żegleń5, Ewa Lewicka14, Maciej Urlik5, Marek Grabka15, Michał Furdal16, Michał Florczyk10, Adam Torbicki10
DOI: 10.33963/KP.a2022.0259
·
Pubmed: 36463573
·
Kardiol Pol 2022;80(11):1169-1181.
Affiliations
  1. 1st Department of Cardiology, Poznan University of Medical Sciences, Poznań, Poland
  2. Department of Cardiac Surgery, Medical University of Gdansk, Gdańsk, Poland
  3. Department of Population Medicine and Lifestyle Diseases Prevention, Medical University of Bialystok, Białystok, Poland
  4. Department of Cardiology, Medical University of Bialystok, Białystok, Poland
  5. Silesian Center for Heart Diseases in Zabrze, Zabrze, Poland
  6. Department of Cardiac, Vascular and Endovascular Surgery and Transplantology, Medical University of Silesia, Katowice, Poland
  7. 1st Department and Chair of Cardiology, Medical University of Lodz, Bieganski Hospital, Łódź, Poland
  8. Department of Pulmonary Circulation, Thromboembolic Diseases and Cardiology, Center of Postgraduate Medical Education, European Health Center, Otwock, Poland
  9. Departament of Cardiology, Institute of Heart Diseases, University Clinical Hospital in Wroclaw, Wrocław, Poland
  10. Pulmonary Circulation Center, Department of Cardiac and Vascular Diseases, John Paul II Hospital in Krakow, Kraków, Poland
  11. Department of Cardiac and Vascular Diseases, Institute of Cardiology, Jagiellonian University Medical College, Kraków, Poland
  12. Departament of Cardiac Surgery, Institute of Heart Diseases, Wroclaw Medical University, Wrocław, Poland
  13. 3rd Department of Cardiology, Faculty of Medical Sciences in Zabrze, Medical University of Silesia, Katowice, Poland
  14. 2nd Department of Cardiology and Heart Electrotherapy Medical University of Gdansk, Gdańsk, Poland
  15. 1st Department of Cardiology, Silesian University of Medicine Katowice, Katowice, Poland
  16. Department of Cardiology, Center for Heart Disease, 4th Military University Hospital in Wroclaw, Wrocław, Poland

open access

Vol 80, No 11 (2022)
Expert opinion
Published online: 2022-11-30

Abstract

Pulmonary arterial hypertension is a rare but progressive disease that leads to death. Modern drug treatment slows the progression of the disease and prolongs patients’ lives, but often, even maximal treatment with parenteral prostacyclin does not prevent deterioration. In the case of inadequate clinical response to drug treatment, lung transplantation (LTx) should be considered. This article aims to analyze thoroughly indications to refer a patient for consultation with a transplant center, the optimal timing of listing for LTx, contraindications for the procedure, bridging techniques, as well as tests needed before and after transplantation. We outline the technique of the procedurę and evaluate psychological aspects of LTx.

Abstract

Pulmonary arterial hypertension is a rare but progressive disease that leads to death. Modern drug treatment slows the progression of the disease and prolongs patients’ lives, but often, even maximal treatment with parenteral prostacyclin does not prevent deterioration. In the case of inadequate clinical response to drug treatment, lung transplantation (LTx) should be considered. This article aims to analyze thoroughly indications to refer a patient for consultation with a transplant center, the optimal timing of listing for LTx, contraindications for the procedure, bridging techniques, as well as tests needed before and after transplantation. We outline the technique of the procedurę and evaluate psychological aspects of LTx.

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Keywords

lung transplantation, pulmonary arterial hypertension, pulmonary arterial hypertension treatment

About this article
Title

Lung transplantation in patients with pulmonary arterial hypertension: The opinion of the Polish Cardiac Society Working Group on Pulmonary Circulation

Journal

Kardiologia Polska (Polish Heart Journal)

Issue

Vol 80, No 11 (2022)

Article type

Expert opinion

Pages

1169-1181

Published online

2022-11-30

Page views

1573

Article views/downloads

223

DOI

10.33963/KP.a2022.0259

Pubmed

36463573

Bibliographic record

Kardiol Pol 2022;80(11):1169-1181.

Keywords

lung transplantation
pulmonary arterial hypertension
pulmonary arterial hypertension treatment

Authors

Tatiana Mularek-Kubzdela
Jacek Wojnarski
Karol Kamiński
Marek Ochman
Jarosław D Kasprzak
Tomasz Stącel
Marcin Kurzyna
Wojciech Karolak
Ewa Mroczek
Grzegorz Kopeć
Roman Przybylski
Ilona Skorzylas
Sławomir Żegleń
Ewa Lewicka
Maciej Urlik
Marek Grabka
Michał Furdal
Michał Florczyk
Adam Torbicki

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