Vol 69, No 11 (2011)
Case studies
Published online: 2011-11-17
The concomitance of pericarditis constrictiva in patient with Silver-Russell syndrome, primary hyperparathyroidism and oncologic history: causal coincidence or pathogenetic sequence?
DOI: 10.33963/v.kp.79495
Kardiol Pol 2011;69(11):1174-1176.
Abstract
The most common cause of calcific pericarditis is idiopathic. We report a case of a 24 year-old woman with Silver-Russell
syndrome, history of Wilms’ tumour in childhood, constrictive pericarditis and primary hyperparathyroidism. We analyse
pathologic mechanisms of disseminated calcification and possible genetic factors that may contribute to aetiology and clinical
presentation of calcific pericarditis.
Kardiol Pol 2011; 69, 11: 1174–1176
Kardiol Pol 2011; 69, 11: 1174–1176
Keywords: pericarditis constrictivacalcificationprimary hyperparathyroidismSilver-Russell syndrome