open access

Vol 74, No 2 (2015)
CASE REPORTS
Published online: 2015-05-28
Submitted: 2015-03-10
Accepted: 2015-03-28
Get Citation

Bilateral large vestibular aqueduct syndrome in an 11-year-old boy. Radiological and clinical findings

T. Przewoźny, K. Markiet, J. Piątkowski
DOI: 10.5603/FM.2015.0022
·
Pubmed: 26050818
·
Folia Morphol 2015;74(2):265-271.

open access

Vol 74, No 2 (2015)
CASE REPORTS
Published online: 2015-05-28
Submitted: 2015-03-10
Accepted: 2015-03-28

Abstract

Clinical observations supplemented with imaging examination show that the large vestibular aqueduct syndrome (LVAS) is a rare developmental anomaly of the inner ear, which leads to hearing loss. The authors present a case history, results of imaging examination (high resolution CT, MRI), results of hearing acuity examinations (tonal audiometry, otoacoustic emissions, brainstem auditory evoked potentials) and results of balance examinations (videonystagmography) in an 11-year-old boy suffering from deep mixed progressive hearing loss of the right ear due to head trauma. The aim of this paper is to specify the most typical clinical, radiological and anatomopathological manifestations of this pathology of the inner ear. The authors describe the diagnostic and identification difficulties associated with the mixed hearing loss observed in this case. The article also discusses the child’s activity limitations, which should be taken into account once diagnosis of this rare labyrinthine pathology is established.

Abstract

Clinical observations supplemented with imaging examination show that the large vestibular aqueduct syndrome (LVAS) is a rare developmental anomaly of the inner ear, which leads to hearing loss. The authors present a case history, results of imaging examination (high resolution CT, MRI), results of hearing acuity examinations (tonal audiometry, otoacoustic emissions, brainstem auditory evoked potentials) and results of balance examinations (videonystagmography) in an 11-year-old boy suffering from deep mixed progressive hearing loss of the right ear due to head trauma. The aim of this paper is to specify the most typical clinical, radiological and anatomopathological manifestations of this pathology of the inner ear. The authors describe the diagnostic and identification difficulties associated with the mixed hearing loss observed in this case. The article also discusses the child’s activity limitations, which should be taken into account once diagnosis of this rare labyrinthine pathology is established.

Get Citation

Keywords

large vestibular aqueduct syndrome, hearing loss, congenital inner ear defect

About this article
Title

Bilateral large vestibular aqueduct syndrome in an 11-year-old boy. Radiological and clinical findings

Journal

Folia Morphologica

Issue

Vol 74, No 2 (2015)

Pages

265-271

Published online

2015-05-28

DOI

10.5603/FM.2015.0022

Pubmed

26050818

Bibliographic record

Folia Morphol 2015;74(2):265-271.

Keywords

large vestibular aqueduct syndrome
hearing loss
congenital inner ear defect

Authors

T. Przewoźny
K. Markiet
J. Piątkowski

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