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Case Reports
Published online: 2019-03-27
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Unusual aberrancy of right coronary artery (RCA) in patient with double-outlet right ventricle (DORV) with pulmonary stenosis (PS)

Santosh Kumar Sinha, Puneet Aggarwal, Lokendra Rekwal, Anupam Kumar Singh, Nishant Kumar Abhishekh, Vinay Krishna
DOI: 10.5603/FC.a2019.0030

open access

Ahead of print
Case Reports
Published online: 2019-03-27

Abstract

The incidence of coronary artery anomalies in double-outlet right ventricle (DORV) or tetralogy of Fallot (TOF) has been reported to be 2% to 10%. Surgical correction in such a scenario, across a narrowed and under-developed right ventricular outflow tract (RVOT), poses a significant challenge and has been associated with increased morbidity and mortality. These combinations at times may change the approach of primary repair to one of initial palliation. Single coronary artery, meaning anomalous origin of the right coronary artery from the left anterior descending artery, is a benign and very rare coronary artery anomaly. Here, we report the case of an 11 year-old boy with double-outlet right ventricle (DORV) with pulmonary stenosis (PS) where pre-operative catheterisation and multi detector CT angiography (MDCT) revealed anomalous right coronary artery arising from left anterior descending artery.

Abstract

The incidence of coronary artery anomalies in double-outlet right ventricle (DORV) or tetralogy of Fallot (TOF) has been reported to be 2% to 10%. Surgical correction in such a scenario, across a narrowed and under-developed right ventricular outflow tract (RVOT), poses a significant challenge and has been associated with increased morbidity and mortality. These combinations at times may change the approach of primary repair to one of initial palliation. Single coronary artery, meaning anomalous origin of the right coronary artery from the left anterior descending artery, is a benign and very rare coronary artery anomaly. Here, we report the case of an 11 year-old boy with double-outlet right ventricle (DORV) with pulmonary stenosis (PS) where pre-operative catheterisation and multi detector CT angiography (MDCT) revealed anomalous right coronary artery arising from left anterior descending artery.

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Keywords

coronary artery anomalies; double-outlet right ventricle; tetralogy of Fallot; anomalous right coronary artery; multi-detector CT angiography

About this article
Title

Unusual aberrancy of right coronary artery (RCA) in patient with double-outlet right ventricle (DORV) with pulmonary stenosis (PS)

Journal

Folia Cardiologica

Issue

Ahead of print

Published online

2019-03-27

DOI

10.5603/FC.a2019.0030

Keywords

coronary artery anomalies
double-outlet right ventricle
tetralogy of Fallot
anomalous right coronary artery
multi-detector CT angiography

Authors

Santosh Kumar Sinha
Puneet Aggarwal
Lokendra Rekwal
Anupam Kumar Singh
Nishant Kumar Abhishekh
Vinay Krishna

References (10)
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