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An uncommon cause of well-known symptoms: acute abdomen in a 2-year-old boy with intestinal malrotation. Case report and literature review
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Afiliacje- Department of Paediatric Surgery, Traumatology and Urology, Poznan University of Medical Sciences, Poznan, Polska
- Student Research Group: Pediatric Surgery; Department of Pediatric Surgery, Traumatology and Urology, Poznan University of Medical Sciences, Poznan, Polska
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Streszczenie
Midgut malrotation is the most frequent congenital defect of the small intestine. The clinical manifestation can vary from being asymptomatic to presenting acutely as volvulus with bilious vomiting.
Presented here is a case of a 32-months-old boy with abdominal pain and several emetic episodes before admission. The patient was diagnosed with ileus and needed emergency surgery which showed the presence of volvulus due to malrotation of the midgut. Extensive partial resections of the jejunum, ileum and colon beginning in the upper part of the rectum up to ascending colon were performed.
Intestinal malrotation is rarely a symptomatic abnormality, however, when it occurs severely it can result in life-threatening complications. Ultrasonography may be a helpful screening tool for early diagnosis, but it needs the experience of the doctor. Treating significant malrotation almost always requires surgery. The timing and urgency depend on the child’s condition.
Streszczenie
Midgut malrotation is the most frequent congenital defect of the small intestine. The clinical manifestation can vary from being asymptomatic to presenting acutely as volvulus with bilious vomiting.
Presented here is a case of a 32-months-old boy with abdominal pain and several emetic episodes before admission. The patient was diagnosed with ileus and needed emergency surgery which showed the presence of volvulus due to malrotation of the midgut. Extensive partial resections of the jejunum, ileum and colon beginning in the upper part of the rectum up to ascending colon were performed.
Intestinal malrotation is rarely a symptomatic abnormality, however, when it occurs severely it can result in life-threatening complications. Ultrasonography may be a helpful screening tool for early diagnosis, but it needs the experience of the doctor. Treating significant malrotation almost always requires surgery. The timing and urgency depend on the child’s condition.
Słowa kluczowe
acute abdomen; child; congenital abnormality; intestinal malrotation; volvulus
Informacje o artykuleTytuł
An uncommon cause of well-known symptoms: acute abdomen in a 2-year-old boy with intestinal malrotation. Case report and literature review
Czasopismo
Numer
Typ artykułu
Opis przypadku
Strony
22-25
Opublikowany online
2022-08-05
Wyświetlenia strony
964
Wyświetlenia/pobrania artykułu
119
DOI
Rekord bibliograficzny
Chirurgia Polska 2022;24(1-2):22-25.
Słowa kluczowe
acute abdomen
child
congenital abnormality
intestinal malrotation
volvulus
Autorzy
Patrycja Sosnowska-Sienkiewicz
Maria Mitkowska
Jakub Langa
Przemysław Mańkowski
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